Q01 ICD-10-CM Code: Encephalocele

A clear reference for the official code description, hierarchy, and related coding information from the FY 2027 U.S. release.

Official description

Q01

Encephalocele

ICD-10-CM diagnosis code · United States clinical modification

Where Q01 sits

  1. 1

    Chapter 17

    Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)

  2. 2

    Section

    Congenital malformations of the nervous system (Q00-Q07)

  3. 3

    Category Q01

    Encephalocele

  4. 4

    Code Q01

    Encephalocele

Codes under Q01

Q01 is a non-billable category. Choose the child code that best matches the documented diagnosis.

Notes for this code

Inclusion terms

No inclusion terms are listed for Q01.

Code first

No “code first” instruction is listed for Q01.

Use additional code

No “use additional code” instruction is listed for Q01.

Excludes1

Conditions that should not be reported together with this code.

  • Meckel-Gruber syndrome (Q61.9)

Excludes2

Conditions not included here that may be reported separately when present.

No Excludes2 note is listed for Q01.

Source and release

Data release
U.S. ICD-10-CM · FY 2027
Effective date
Oct 1, 2026

This reference is generated from Vero’s ICD-10-CM description, hierarchy, and code-note dataset. The visible content and structured data share that source.

Frequently asked questions

What does ICD-10-CM code Q01 mean?

Q01 is the FY 2027 U.S. ICD-10-CM code for “Encephalocele.”

Is Q01 a billable or specific ICD-10-CM code?

No. Q01 has more specific child codes in the FY 2027 reference data. Select the code that matches the documentation and confirm the active code set and payer requirements.

Where is Q01 located in ICD-10-CM?

Q01 is listed in Chapter 17, Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1), within Congenital malformations of the nervous system (Q00-Q07) (Q00–Q07), under category Q01, Encephalocele.

What coding notes are listed for Q01?

No inclusion terms are listed for Q01 in this reference record. No code-first instruction is listed. Excludes1 notes: Meckel-Gruber syndrome (Q61.9). No Excludes2 note is listed.