U.S. ICD-10-CM · FY 2027

Q00 ICD-10-CM Code: Anencephaly and similar malformations

A clear reference for the official code description, hierarchy, and related coding information from the FY 2027 U.S. release.

Code definition

Official description

Q00

Anencephaly and similar malformations

ICD-10-CM diagnosis code · United States clinical modification

Classification

Where Q00 sits

  1. 1

    Chapter 17

    Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)

  2. 2

    Section

    Congenital malformations of the nervous system (Q00-Q07)

  3. 3

    Category Q00

    Anencephaly and similar malformations

  4. 4

    Code Q00

    Anencephaly and similar malformations

More specific choices

Codes under Q00

Q00 is a non-billable category. Choose the child code that best matches the documented diagnosis.

Documentation details

Notes for this code

Inclusion terms

No inclusion terms are listed for Q00.

Code first

No “code first” instruction is listed for Q00.

Use additional code

No “use additional code” instruction is listed for Q00.

Excludes1

Conditions that should not be reported together with this code.

No Excludes1 note is listed for Q00.

Excludes2

Conditions not included here that may be reported separately when present.

No Excludes2 note is listed for Q00.

Transparency

Source and release

Data release

U.S. ICD-10-CM · FY 2027

Effective date

Oct 1, 2026

This reference is generated from Vero’s ICD-10-CM description, hierarchy, and code-note dataset. The visible content and structured data share that source.

Review the CDC/NCHS ICD-10-CM source

Code-specific guidance

Frequently asked questions

What does ICD-10-CM code Q00 mean?

Q00 is the FY 2027 U.S. ICD-10-CM code for “Anencephaly and similar malformations.”

Is Q00 a billable or specific ICD-10-CM code?

No. Q00 has more specific child codes in the FY 2027 reference data. Select the code that matches the documentation and confirm the active code set and payer requirements.

Where is Q00 located in ICD-10-CM?

Q00 is listed in Chapter 17, Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1), within Congenital malformations of the nervous system (Q00-Q07) (Q00–Q07), under category Q00, Anencephaly and similar malformations.

What coding notes are listed for Q00?

No inclusion terms are listed for Q00 in this reference record. No code-first instruction is listed. No Excludes1 note is listed. No Excludes2 note is listed.

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