N01 ICD-10-CM Code: Rapidly progressive nephritic syndrome
A clear reference for the official code description, hierarchy, and related coding information from the FY 2027 U.S. release.
Official description
N01Rapidly progressive nephritic syndrome
ICD-10-CM diagnosis code · United States clinical modification
Where N01 sits
- 1
Chapter 14
Diseases of the genitourinary system (N00-N99)
- 2
Section
Glomerular diseases (N00-N08)
- 3
Category N01
Rapidly progressive nephritic syndrome
- 4
Code N01
Rapidly progressive nephritic syndrome
Codes under N01
N01 is a non-billable category. Choose the child code that best matches the documented diagnosis.
N01.0Rapidly progressive nephritic syndrome with minor glomerular abnormalityN01.1Rapidly progressive nephritic syndrome with focal and segmental glomerular lesionsN01.2Rapidly progressive nephritic syndrome with diffuse membranous glomerulonephritisN01.3Rapidly progressive nephritic syndrome with diffuse mesangial proliferative glomerulonephritisN01.4Rapidly progressive nephritic syndrome with diffuse endocapillary proliferative glomerulonephritisN01.5Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritisN01.6Rapidly progressive nephritic syndrome with dense deposit diseaseN01.7Rapidly progressive nephritic syndrome with diffuse crescentic glomerulonephritisN01.8Rapidly progressive nephritic syndrome with other morphologic changesN01.9Rapidly progressive nephritic syndrome with unspecified morphologic changesN01.ARapidly progressive nephritic syndrome with C3 glomerulonephritisNotes for this code
Inclusion terms
No inclusion terms are listed for N01.
Code first
No “code first” instruction is listed for N01.
Use additional code
No “use additional code” instruction is listed for N01.
Excludes1
Conditions that should not be reported together with this code.
- nephritic syndrome NOS (N05.-)
Excludes2
Conditions not included here that may be reported separately when present.
No Excludes2 note is listed for N01.
Source and release
- Data release
- U.S. ICD-10-CM · FY 2027
- Effective date
- Oct 1, 2026
- Publisher
- Vero Scribe Inc.
This reference is generated from Vero’s ICD-10-CM description, hierarchy, and code-note dataset. The visible content and structured data share that source.
Frequently asked questions
What does ICD-10-CM code N01 mean?
N01 is the FY 2027 U.S. ICD-10-CM code for “Rapidly progressive nephritic syndrome.”
Is N01 a billable or specific ICD-10-CM code?
No. N01 has more specific child codes in the FY 2027 reference data. Select the code that matches the documentation and confirm the active code set and payer requirements.
Where is N01 located in ICD-10-CM?
N01 is listed in Chapter 14, Diseases of the genitourinary system (N00-N99), within Glomerular diseases (N00-N08) (N00–N08), under category N01, Rapidly progressive nephritic syndrome.
What coding notes are listed for N01?
No inclusion terms are listed for N01 in this reference record. No code-first instruction is listed. Excludes1 notes: nephritic syndrome NOS (N05.-). No Excludes2 note is listed.