U.S. ICD-10-CM · FY 2027

N01 ICD-10-CM Code: Rapidly progressive nephritic syndrome

A clear reference for the official code description, hierarchy, and related coding information from the FY 2027 U.S. release.

Code definition

Official description

N01

Rapidly progressive nephritic syndrome

ICD-10-CM diagnosis code · United States clinical modification

Classification

Where N01 sits

  1. 1

    Chapter 14

    Diseases of the genitourinary system (N00-N99)

  2. 2

    Section

    Glomerular diseases (N00-N08)

  3. 3

    Category N01

    Rapidly progressive nephritic syndrome

  4. 4

    Code N01

    Rapidly progressive nephritic syndrome

More specific choices

Codes under N01

N01 is a non-billable category. Choose the child code that best matches the documented diagnosis.

N01.0

Rapidly progressive nephritic syndrome with minor glomerular abnormality

N01.1

Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions

N01.2

Rapidly progressive nephritic syndrome with diffuse membranous glomerulonephritis

N01.3

Rapidly progressive nephritic syndrome with diffuse mesangial proliferative glomerulonephritis

N01.4

Rapidly progressive nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis

N01.5

Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritis

N01.6

Rapidly progressive nephritic syndrome with dense deposit disease

N01.7

Rapidly progressive nephritic syndrome with diffuse crescentic glomerulonephritis

N01.8

Rapidly progressive nephritic syndrome with other morphologic changes

N01.9

Rapidly progressive nephritic syndrome with unspecified morphologic changes

N01.A

Rapidly progressive nephritic syndrome with C3 glomerulonephritis

Documentation details

Notes for this code

Inclusion terms

No inclusion terms are listed for N01.

Code first

No “code first” instruction is listed for N01.

Use additional code

No “use additional code” instruction is listed for N01.

Excludes1

Conditions that should not be reported together with this code.

  • nephritic syndrome NOS (N05.-)

Excludes2

Conditions not included here that may be reported separately when present.

No Excludes2 note is listed for N01.

Transparency

Source and release

Data release

U.S. ICD-10-CM · FY 2027

Effective date

Oct 1, 2026

Publisher

Vero Scribe Inc.

This reference is generated from Vero’s ICD-10-CM description, hierarchy, and code-note dataset. The visible content and structured data share that source.

Review the CDC/NCHS ICD-10-CM source

Code-specific guidance

Frequently asked questions

What does ICD-10-CM code N01 mean?

N01 is the FY 2027 U.S. ICD-10-CM code for “Rapidly progressive nephritic syndrome.”

Is N01 a billable or specific ICD-10-CM code?

No. N01 has more specific child codes in the FY 2027 reference data. Select the code that matches the documentation and confirm the active code set and payer requirements.

Where is N01 located in ICD-10-CM?

N01 is listed in Chapter 14, Diseases of the genitourinary system (N00-N99), within Glomerular diseases (N00-N08) (N00–N08), under category N01, Rapidly progressive nephritic syndrome.

What coding notes are listed for N01?

No inclusion terms are listed for N01 in this reference record. No code-first instruction is listed. Excludes1 notes: nephritic syndrome NOS (N05.-). No Excludes2 note is listed.

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