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N01 ICD-10-CA category: Rapidly progressive nephritic syndrome

N01 isn’t a code on its own. Choose one of the 10 codes beneath it, the one the documentation supports.

Official description

N01

Rapidly progressive nephritic syndrome

ICD-10-CA · Canada

Codes in N01

N01 isn’t a code on its own. Open the code that matches what the note documents.

N01.0Rapidly progressive nephritic syndrome, minor glomerular abnormalityN01.1Rapidly progressive nephritic syndrome, focal and segmental glomerular lesionsN01.2Rapidly progressive nephritic syndrome, diffuse membranous glomerulonephritisN01.3Rapidly progressive nephritic syndrome, diffuse mesangial proliferative glomerulonephritisN01.4Rapidly progressive nephritic syndrome, diffuse endocapillary proliferative glomerulonephritisN01.5Rapidly progressive nephritic syndrome, diffuse mesangiocapillary glomerulonephritisN01.6Rapidly progressive nephritic syndrome, dense deposit diseaseN01.7Rapidly progressive nephritic syndrome, diffuse crescentic glomerulonephritisN01.8Rapidly progressive nephritic syndrome, otherN01.9Rapidly progressive nephritic syndrome, unspecified

Notes for N01

As CIHI prints them, with any note N01 takes from the headings above it.

Includes

  • Rapidly progressive:• glomerular disease• glomerulonephritis• nephritis

Use additional code

Add a code for this detail when the note documents it.

Excludes

Conditions classified elsewhere.

  • Nephritic syndrome NOS (N05.-)
  • Hypertensive renal disease (I12)From N00-N08 Glomerular diseases
  • Certain conditions originating in the perinatal period (P00-P96)certain infectious and parasitic diseases (A00-B99)complications of pregnancy, childbirth and the puerperium (O00-O99)congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)endocrine, nutritional and metabolic diseases (E00-E90)injury, poisoning and certain other consequences of external causes (S00-T98)neoplasms (C00-D48)symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R99)From Chapter 14: Diseases of the genitourinary system (N00-N99)

Note

  • See note under chapter heading (N00-N08) for fourth character subdivisions
  • The following fourth-character subdivisions classify morphological changes and are for use with categories N00 - N07. Subdivisions .0 - .8 should not normally be used unless these have been specifically identified (e.g. by renal biopsy or autopsy). The three-character categories relate to clinical syndromes..0 Minor glomerular abnormalityMinimal change lesion.1 Focal and segmental glomerular lesionsGlomerulonephritis, Hyalinosis, Sclerosis — focal and segmental.2 Diffuse membranous glomerulonephritis.3 Diffuse mesangial proliferative glomerulonephritis.4 Diffuse endocapillary proliferative glomerulonephritis.5 Diffuse mesangiocapillary glomerulonephritisMembranoproliferative glomerulonephritis, types 1 and 3, or NOS.6 Dense deposit diseaseMembranoproliferative glomerulonephritis, type 2.7 Diffuse crescentic glomerulonephritisExtracapillary glomerulonephritis.8 OtherProliferative glomerulonephritis NOS.9 UnspecifiedFrom N00-N08 Glomerular diseases

Where N01 sits

  1. 1ChapterChapter 14: Diseases of the genitourinary system (N00-N99)
  2. 2Block N00-N08Glomerular diseases
  3. 3Category N01Rapidly progressive nephritic syndrome

Source and release

Data release
ICD-10-CA · FY 2026–2027
Effective date
Apr 1, 2026
Publisher
CIHI

This page is built from the ICD-10-CA catalog that Vero Codes reads when it suggests codes: Canadian Institute for Health Information’s FY 2026–2027 release, imported from the publisher’s file and checked against it. The description, notes and structured data come from the same record.

See N01 in the CIHI source

Frequently asked questions

Is N01 a valid ICD-10-CA code?

No. N01 (Rapidly progressive nephritic syndrome) is a category heading in CIHI’s ICD-10-CA FY 2026–2027 release. It holds 10 codes; record the one the documentation supports.

Where is N01 in ICD-10-CA?

N01 sits under N00-N08 Glomerular diseases, within Chapter 14: Diseases of the genitourinary system (N00-N99).

What coding notes apply to N01?

ICD-10-CA lists Note, Includes, Excludes, Use additional code notes for N01, including those from the headings it sits under. They are listed on this page with where each one comes from.

Which ICD-10-CA release does this page use?

It uses CIHI’s FY 2026–2027 release, in effect from Apr 1, 2026 to Mar 31, 2027. It is a reference: confirm the code against the current list and the payer’s rules before you submit it.

Codes beside N01

N00Acute nephritic syndromeN02Recurrent and persistent haematuriaN03Chronic nephritic syndromeN04Nephrotic syndromeN05Unspecified nephritic syndromeN06Isolated proteinuria with specified morphological lesionN07Hereditary nephropathy, not elsewhere classifiedN08Glomerular disorders in diseases classified elsewhere