N01.1 ICD-10-CA code: Rapidly progressive nephritic syndrome, focal and segmental glomerular lesions

N01.1 is the ICD-10-CA code for “Rapidly progressive nephritic syndrome, focal and segmental glomerular lesions” in CIHI’s FY 2026–2027 release, in effect from Apr 1, 2026.

Official description

N01.1

Rapidly progressive nephritic syndrome, focal and segmental glomerular lesions

Short description: Progress neph syndr focl seg glom lesion

ICD-10-CA · Canada · Also written N011

Notes for N01.1

As CIHI prints them, with any note N01.1 takes from the headings above it.

Includes

Focal:• and segmental• hyalinosis• sclerosis• glomerulonephritis
Rapidly progressive:• glomerular disease• glomerulonephritis• nephritisFrom N01 Rapidly progressive nephritic syndrome

Use additional code

Add a code for this detail when the note documents it.

Use additional code to identify associated chronic kidney disease (N18.-)From N00-N08 Glomerular diseases
Use additional code to identify external cause (Chapter XX) or presence of renal failure, Acute (N17) or Unspecified (N19)From N00-N08 Glomerular diseases

Excludes

Conditions classified elsewhere.

Nephritic syndrome NOS (N05.-)From N01 Rapidly progressive nephritic syndrome
Hypertensive renal disease (I12)From N00-N08 Glomerular diseases
Certain conditions originating in the perinatal period (P00-P96)certain infectious and parasitic diseases (A00-B99)complications of pregnancy, childbirth and the puerperium (O00-O99)congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)endocrine, nutritional and metabolic diseases (E00-E90)injury, poisoning and certain other consequences of external causes (S00-T98)neoplasms (C00-D48)symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R99)From Chapter 14: Diseases of the genitourinary system (N00-N99)

Note

See note under chapter heading (N00-N08) for fourth character subdivisionsFrom N01 Rapidly progressive nephritic syndrome
The following fourth-character subdivisions classify morphological changes and are for use with categories N00 - N07. Subdivisions .0 - .8 should not normally be used unless these have been specifically identified (e.g. by renal biopsy or autopsy). The three-character categories relate to clinical syndromes..0 Minor glomerular abnormalityMinimal change lesion.1 Focal and segmental glomerular lesionsGlomerulonephritis, Hyalinosis, Sclerosis — focal and segmental.2 Diffuse membranous glomerulonephritis.3 Diffuse mesangial proliferative glomerulonephritis.4 Diffuse endocapillary proliferative glomerulonephritis.5 Diffuse mesangiocapillary glomerulonephritisMembranoproliferative glomerulonephritis, types 1 and 3, or NOS.6 Dense deposit diseaseMembranoproliferative glomerulonephritis, type 2.7 Diffuse crescentic glomerulonephritisExtracapillary glomerulonephritis.8 OtherProliferative glomerulonephritis NOS.9 UnspecifiedFrom N00-N08 Glomerular diseases

Where N01.1 sits

1ChapterChapter 14: Diseases of the genitourinary system (N00-N99)
2Block N00-N08Glomerular diseases
3Category N01Rapidly progressive nephritic syndrome
4Valid code N01.1Rapidly progressive nephritic syndrome, focal and segmental glomerular lesions

Source and release

Data release: ICD-10-CA · FY 2026–2027
Effective date: Apr 1, 2026
Publisher: CIHI

This page is built from the ICD-10-CA catalog that Vero Codes reads when it suggests codes: Canadian Institute for Health Information’s FY 2026–2027 release, imported from the publisher’s file and checked against it. The description, notes and structured data come from the same record.

See N01.1 in the CIHI source

Frequently asked questions

What does ICD-10-CA code N01.1 mean?

N01.1 is the ICD-10-CA code for “Rapidly progressive nephritic syndrome, focal and segmental glomerular lesions” in CIHI’s ICD-10-CA FY 2026–2027 release.

Where is N01.1 in ICD-10-CA?

N01.1 sits under N01 Rapidly progressive nephritic syndrome, within N00-N08 Glomerular diseases, within Chapter 14: Diseases of the genitourinary system (N00-N99).

What coding notes apply to N01.1?

ICD-10-CA lists Includes, Note, Excludes, Use additional code notes for N01.1, including those from the headings it sits under. They are listed on this page with where each one comes from.

Which ICD-10-CA release does this page use?

It uses CIHI’s FY 2026–2027 release, in effect from Apr 1, 2026 to Mar 31, 2027. It is a reference: confirm the code against the current list and the payer’s rules before you submit it.

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