N04 ICD-10-CA category: Nephrotic syndrome
N04 isn’t a code on its own. Choose one of the 10 codes beneath it, the one the documentation supports.
Official description
N04Nephrotic syndrome
ICD-10-CA · Canada
Codes in N04
N04 isn’t a code on its own. Open the code that matches what the note documents.
N04.0Nephrotic syndrome, minor glomerular abnormalityN04.1Nephrotic syndrome, focal and segmental glomerular lesionsN04.2Nephrotic syndrome, diffuse membranous glomerulonephritisN04.3Nephrotic syndrome, diffuse mesangial proliferative glomerulonephritisN04.4Nephrotic syndrome, diffuse endocapillary proliferative glomerulonephritisN04.5Nephrotic syndrome, diffuse mesangiocapillary glomerulonephritisN04.6Nephrotic syndrome, dense deposit diseaseN04.7Nephrotic syndrome, diffuse crescentic glomerulonephritisN04.8Nephrotic syndrome, otherN04.9Nephrotic syndrome, unspecifiedNotes for N04
As CIHI prints them, with any note N04 takes from the headings above it.
Includes
- Congenital nephrotic syndromelipoid nephrosis
Use additional code
Add a code for this detail when the note documents it.
- Use additional code to identify associated chronic kidney disease (N18.-)From N00-N08 Glomerular diseases
- Use additional code to identify external cause (Chapter XX) or presence of renal failure, Acute (N17) or Unspecified (N19)From N00-N08 Glomerular diseases
Excludes
Conditions classified elsewhere.
- Hypertensive renal disease (I12)From N00-N08 Glomerular diseases
- Certain conditions originating in the perinatal period (P00-P96)certain infectious and parasitic diseases (A00-B99)complications of pregnancy, childbirth and the puerperium (O00-O99)congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)endocrine, nutritional and metabolic diseases (E00-E90)injury, poisoning and certain other consequences of external causes (S00-T98)neoplasms (C00-D48)symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R99)From Chapter 14: Diseases of the genitourinary system (N00-N99)
Note
- See note under chapter heading (N00-N08) for fourth character subdivisions
- The following fourth-character subdivisions classify morphological changes and are for use with categories N00 - N07. Subdivisions .0 - .8 should not normally be used unless these have been specifically identified (e.g. by renal biopsy or autopsy). The three-character categories relate to clinical syndromes..0 Minor glomerular abnormalityMinimal change lesion.1 Focal and segmental glomerular lesionsGlomerulonephritis, Hyalinosis, Sclerosis — focal and segmental.2 Diffuse membranous glomerulonephritis.3 Diffuse mesangial proliferative glomerulonephritis.4 Diffuse endocapillary proliferative glomerulonephritis.5 Diffuse mesangiocapillary glomerulonephritisMembranoproliferative glomerulonephritis, types 1 and 3, or NOS.6 Dense deposit diseaseMembranoproliferative glomerulonephritis, type 2.7 Diffuse crescentic glomerulonephritisExtracapillary glomerulonephritis.8 OtherProliferative glomerulonephritis NOS.9 UnspecifiedFrom N00-N08 Glomerular diseases
Where N04 sits
- 1ChapterChapter 14: Diseases of the genitourinary system (N00-N99)
- 2Block N00-N08Glomerular diseases
- 3Category N04Nephrotic syndrome
Source and release
- Data release
- ICD-10-CA · FY 2026–2027
- Effective date
- Apr 1, 2026
- Publisher
- CIHI
This page is built from the ICD-10-CA catalog that Vero Codes reads when it suggests codes: Canadian Institute for Health Information’s FY 2026–2027 release, imported from the publisher’s file and checked against it. The description, notes and structured data come from the same record.
Frequently asked questions
Is N04 a valid ICD-10-CA code?
No. N04 (Nephrotic syndrome) is a category heading in CIHI’s ICD-10-CA FY 2026–2027 release. It holds 10 codes; record the one the documentation supports.
Where is N04 in ICD-10-CA?
N04 sits under N00-N08 Glomerular diseases, within Chapter 14: Diseases of the genitourinary system (N00-N99).
What coding notes apply to N04?
ICD-10-CA lists Note, Includes, Use additional code, Excludes notes for N04, including those from the headings it sits under. They are listed on this page with where each one comes from.
Which ICD-10-CA release does this page use?
It uses CIHI’s FY 2026–2027 release, in effect from Apr 1, 2026 to Mar 31, 2027. It is a reference: confirm the code against the current list and the payer’s rules before you submit it.
Codes beside N04
View N00-N08N00Acute nephritic syndromeN01Rapidly progressive nephritic syndromeN02Recurrent and persistent haematuriaN03Chronic nephritic syndromeN05Unspecified nephritic syndromeN06Isolated proteinuria with specified morphological lesionN07Hereditary nephropathy, not elsewhere classifiedN08Glomerular disorders in diseases classified elsewhere