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Q87.0 ICD-10-CA code: Congenital malformation syndromes predominantly affecting facial appearance

Q87.0 is the ICD-10-CA code for “Congenital malformation syndromes predominantly affecting facial appearance” in CIHI’s FY 2026–2027 release, in effect from Apr 1, 2026.

Official description

Q87.0

Congenital malformation syndromes predominantly affecting facial appearance

Short description: Congen syndr predom aff facial appear

ICD-10-CA · Canada · Also written Q870

Index terms

Entries in CIHI’s alphabetical index that lead to Q87.0. Searching the index by the condition the note names is how coders reach this code.

  • Cyclopism
  • Whistling face
  • Apert's syndrome
  • Cyclopia, cyclops
  • Fraser's syndrome
  • Moebius, syndrome
  • Hanhart's syndrome
  • Carpenter's syndrome
  • Syndrome, first arch
  • Acrocephalosyndactyly
  • Coffin Lowry syndrome
  • Robin(Pierre) syndrome
  • Dyscranio pygo phalangy
  • Freeman Sheldon syndrome
  • Syndrome, whistling face
  • Acrocephalopolysyndactyly
  • Cryptophthalmos, syndrome
  • Syndrome, cryptophthalmos
  • Goldenhar(Gorlin) syndrome
  • Hallerman Streiff syndrome
  • Williams (Bueren) syndrome
  • Aglossia adactylia syndrome
  • Marchesani (Weill) syndrome
  • Ullrich Feichtiger syndrome
  • Dysplasia, oculodentodigital
  • Gorlin Chaudry Moss syndrome
  • Syndrome, oro facial digital
  • Syndrome, oto palatal digital
  • Tower skull, with exophthalmos
  • Syndrome, eyelid malar mandible
  • Mohr's syndrome (types I and II)
  • Papillon Leage and Psaume syndrome
  • Pierre Robin deformity or syndrome
  • Syndrome, micrognathia glossoptosis
  • Syndrome, congenital, facial diplegia
  • Meyer Schwickerath and Weyer's syndrome
  • Syndrome, congenital, oculo auriculovertebral
  • Syndrome, congenital, oculofacial diplegia (Moebius)
  • Moebius, syndrome, congenital oculofacial paralysis (with other anomalies)
  • Paralysis, paralytic (complete) (incomplete), oculofacial, congenital (Moebius)

Notes for Q87.0

As CIHI prints them, with any note Q87.0 takes from the headings above it.

Includes

  • AcrocephalopolysyndactylyAcrocephalosyndactyly [Apert]Coffin-Lowry syndromeCryptophthalmos syndromeCyclopiaSyndrome:• Goldenhar• Moebius• oro-facial-digital• RobinWhistling faceWilliams-(Beuren) syndrome

Excludes

Conditions classified elsewhere.

  • Inborn errors of metabolism (E70-E90)From Chapter 17: Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)

Where Q87.0 sits

  1. 1ChapterChapter 17: Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
  2. 2Block Q80-Q89Other congenital malformations
  3. 3Category Q87Other specified congenital malformation syndromes affecting multiple systems
  4. 4Valid code Q87.0Congenital malformation syndromes predominantly affecting facial appearance

Source and release

Data release
ICD-10-CA · FY 2026–2027
Effective date
Apr 1, 2026
Publisher
CIHI

This page is built from the ICD-10-CA catalog that Vero Codes reads when it suggests codes: Canadian Institute for Health Information’s FY 2026–2027 release, imported from the publisher’s file and checked against it. The description, notes and structured data come from the same record.

See Q87.0 in the CIHI source

Frequently asked questions

What does ICD-10-CA code Q87.0 mean?

Q87.0 is the ICD-10-CA code for “Congenital malformation syndromes predominantly affecting facial appearance” in CIHI’s ICD-10-CA FY 2026–2027 release.

Where is Q87.0 in ICD-10-CA?

Q87.0 sits under Q87 Other specified congenital malformation syndromes affecting multiple systems, within Q80-Q89 Other congenital malformations, within Chapter 17: Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99).

What coding notes apply to Q87.0?

ICD-10-CA lists Includes, Excludes notes for Q87.0, including those from the headings it sits under. They are listed on this page with where each one comes from.

Which ICD-10-CA release does this page use?

It uses CIHI’s FY 2026–2027 release, in effect from Apr 1, 2026 to Mar 31, 2027. It is a reference: confirm the code against the current list and the payer’s rules before you submit it.

Codes beside Q87.0

Q87.1Congenital malformation syndromes predominantly associated with short statureQ87.2Congenital malformation syndromes predominantly involving limbsQ87.3Congenital malformation syndromes involving early overgrowthQ87.4Marfan's syndromeQ87.5Other congenital malformation syndromes with other skeletal changesQ87.8Other specified congenital malformation syndromes, not elsewhere classified