Q85.8 ICD-10-CA code: Other phakomatoses, not elsewhere classified

Q85.8 is the ICD-10-CA code for “Other phakomatoses, not elsewhere classified” in CIHI’s FY 2026–2027 release, in effect from Apr 1, 2026.

Official description

Q85.8

Other phakomatoses, not elsewhere classified

Short description: Other phakomatoses NEC

ICD-10-CA · Canada · Also written Q858

Index terms

Entries in CIHI’s alphabetical index that lead to Q85.8. Searching the index by the condition the note names is how coders reach this code.

  • Hippel's disease
  • Kraft Weber Dimitri disease
  • Lindau (von Hippel) disease
  • Phakomatosis, specified NEC
  • Dimitri Sturge Weber disease
  • Angiomatosis, encephalotrigeminal
  • Peutz Jeghers disease or syndrome
  • Von Hippel(Lindau) disease or syndrome
  • Sturge(Weber)(Dimitri)(Kalischer) disease or syndrome

Notes for Q85.8

As CIHI prints them, with any note Q85.8 takes from the headings above it.

Includes

  • Syndrome:• Peutz-Jeghers• Sturge-Weber(-Dimitri)• von Hippel-Lindau

Excludes

Conditions classified elsewhere.

  • Meckel-Gruber syndrome (Q61.9)
  • Ataxia telangiectasia [Louis-Bar] (G11.3)familial dysautonomia [Riley-Day] (G90.1)From Q85 Phakomatoses, not elsewhere classified
  • Inborn errors of metabolism (E70-E90)From Chapter 17: Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)

Where Q85.8 sits

  1. 1ChapterChapter 17: Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
  2. 2Block Q80-Q89Other congenital malformations
  3. 3Category Q85Phakomatoses, not elsewhere classified
  4. 4Valid code Q85.8Other phakomatoses, not elsewhere classified

Source and release

Data release
ICD-10-CA · FY 2026–2027
Effective date
Apr 1, 2026
Publisher
CIHI

This page is built from the ICD-10-CA catalog that Vero Codes reads when it suggests codes: Canadian Institute for Health Information’s FY 2026–2027 release, imported from the publisher’s file and checked against it. The description, notes and structured data come from the same record.

Frequently asked questions

What does ICD-10-CA code Q85.8 mean?

Q85.8 is the ICD-10-CA code for “Other phakomatoses, not elsewhere classified” in CIHI’s ICD-10-CA FY 2026–2027 release.

Where is Q85.8 in ICD-10-CA?

Q85.8 sits under Q85 Phakomatoses, not elsewhere classified, within Q80-Q89 Other congenital malformations, within Chapter 17: Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99).

What coding notes apply to Q85.8?

ICD-10-CA lists Includes, Excludes notes for Q85.8, including those from the headings it sits under. They are listed on this page with where each one comes from.

Which ICD-10-CA release does this page use?

It uses CIHI’s FY 2026–2027 release, in effect from Apr 1, 2026 to Mar 31, 2027. It is a reference: confirm the code against the current list and the payer’s rules before you submit it.