Q80.4 ICD-10-CA code: Harlequin fetus

Q80.4 is the ICD-10-CA code for “Harlequin fetus” in CIHI’s FY 2026–2027 release, in effect from Apr 1, 2026.

Official description

Q80.4

Harlequin fetus

ICD-10-CA · Canada · Also written Q804

Index terms

Entries in CIHI’s alphabetical index that lead to Q80.4. Searching the index by the condition the note names is how coders reach this code.

  • Harlequin (fetus)
  • Ichthyosis (congenital), fetalis

Notes for Q80.4

As CIHI prints them, with any note Q80.4 takes from the headings above it.

Excludes

Conditions classified elsewhere.

  • Refsum's disease (G60.1)From Q80 Congenital ichthyosis
  • Inborn errors of metabolism (E70-E90)From Chapter 17: Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)

Where Q80.4 sits

  1. 1ChapterChapter 17: Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
  2. 2Block Q80-Q89Other congenital malformations
  3. 3Category Q80Congenital ichthyosis
  4. 4Valid code Q80.4Harlequin fetus

Source and release

Data release
ICD-10-CA · FY 2026–2027
Effective date
Apr 1, 2026
Publisher
CIHI

This page is built from the ICD-10-CA catalog that Vero Codes reads when it suggests codes: Canadian Institute for Health Information’s FY 2026–2027 release, imported from the publisher’s file and checked against it. The description, notes and structured data come from the same record.

Frequently asked questions

What does ICD-10-CA code Q80.4 mean?

Q80.4 is the ICD-10-CA code for “Harlequin fetus” in CIHI’s ICD-10-CA FY 2026–2027 release.

Where is Q80.4 in ICD-10-CA?

Q80.4 sits under Q80 Congenital ichthyosis, within Q80-Q89 Other congenital malformations, within Chapter 17: Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99).

What coding notes apply to Q80.4?

ICD-10-CA lists Excludes notes for Q80.4, including those from the headings it sits under. They are listed on this page with where each one comes from.

Which ICD-10-CA release does this page use?

It uses CIHI’s FY 2026–2027 release, in effect from Apr 1, 2026 to Mar 31, 2027. It is a reference: confirm the code against the current list and the payer’s rules before you submit it.