Q03.0 ICD-10-CA code: Malformations of aqueduct of Sylvius
Q03.0 is the ICD-10-CA code for “Malformations of aqueduct of Sylvius” in CIHI’s FY 2026–2027 release, in effect from Apr 1, 2026.
Official description
Q03.0Malformations of aqueduct of Sylvius
ICD-10-CA · Canada · Also written Q030
Index terms
Entries in CIHI’s alphabetical index that lead to Q03.0. Searching the index by the condition the note names is how coders reach this code.
- Atresia, atretic, aqueduct of Sylvius
- Stricture, aqueduct of Sylvius (congenital)
- Septum, septate (congenital), aqueduct of Sylvius
- Occlusion, occluded, aqueduct of Sylvius, congenital
- Stenosis (cicatricial), aqueduct of Sylvius (congenital)
- Obstruction, obstructed, obstructive, aqueduct of Sylvius, congenital
- Anomaly, anomalous (congenital) (unspecified type), aqueduct of Sylvius
- Hydrocephalus (acquired) (external) (internal) (malignant) (recurrent), aqueduct Sylvius stricture
Notes for Q03.0
As CIHI prints them, with any note Q03.0 takes from the headings above it.
Includes
- Aqueduct of Sylvius:• anomaly• obstruction, congenital• stenosis
- Hydrocephalus in newbornFrom Q03 Congenital hydrocephalus
Excludes
Conditions classified elsewhere.
- Arnold-Chiari syndrome (Q07.0)hydrocephalus:• acquired NOS (G91.-)• acquired, of newborn (P91.7)• due to congenital toxoplasmosis (P37.1)• with spina bifida (Q05.0-Q05.4)From Q03 Congenital hydrocephalus
- Inborn errors of metabolism (E70-E90)From Chapter 17: Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
Where Q03.0 sits
- 1ChapterChapter 17: Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- 2Block Q00-Q07Congenital malformations of the nervous system
- 3Category Q03Congenital hydrocephalus
- 4Valid code Q03.0Malformations of aqueduct of Sylvius
Source and release
- Data release
- ICD-10-CA · FY 2026–2027
- Effective date
- Apr 1, 2026
- Publisher
- CIHI
This page is built from the ICD-10-CA catalog that Vero Codes reads when it suggests codes: Canadian Institute for Health Information’s FY 2026–2027 release, imported from the publisher’s file and checked against it. The description, notes and structured data come from the same record.
Frequently asked questions
What does ICD-10-CA code Q03.0 mean?
Q03.0 is the ICD-10-CA code for “Malformations of aqueduct of Sylvius” in CIHI’s ICD-10-CA FY 2026–2027 release.
Where is Q03.0 in ICD-10-CA?
Q03.0 sits under Q03 Congenital hydrocephalus, within Q00-Q07 Congenital malformations of the nervous system, within Chapter 17: Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99).
What coding notes apply to Q03.0?
ICD-10-CA lists Includes, Excludes notes for Q03.0, including those from the headings it sits under. They are listed on this page with where each one comes from.
Which ICD-10-CA release does this page use?
It uses CIHI’s FY 2026–2027 release, in effect from Apr 1, 2026 to Mar 31, 2027. It is a reference: confirm the code against the current list and the payer’s rules before you submit it.