Q00 ICD-10-CA category: Anencephaly and similar malformations
Q00 isn’t a code on its own. Choose one of the 3 codes beneath it, the one the documentation supports.
Official description
Q00Anencephaly and similar malformations
ICD-10-CA · Canada
Codes in Q00
Q00 isn’t a code on its own. Open the code that matches what the note documents.
Notes for Q00
As CIHI prints them, with any note Q00 takes from the headings above it.
Excludes
Conditions classified elsewhere.
- Inborn errors of metabolism (E70-E90)From Chapter 17: Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
Where Q00 sits
- 1ChapterChapter 17: Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- 2Block Q00-Q07Congenital malformations of the nervous system
- 3Category Q00Anencephaly and similar malformations
Source and release
- Data release
- ICD-10-CA · FY 2026–2027
- Effective date
- Apr 1, 2026
- Publisher
- CIHI
This page is built from the ICD-10-CA catalog that Vero Codes reads when it suggests codes: Canadian Institute for Health Information’s FY 2026–2027 release, imported from the publisher’s file and checked against it. The description, notes and structured data come from the same record.
Frequently asked questions
Is Q00 a valid ICD-10-CA code?
No. Q00 (Anencephaly and similar malformations) is a category heading in CIHI’s ICD-10-CA FY 2026–2027 release. It holds 3 codes; record the one the documentation supports.
Where is Q00 in ICD-10-CA?
Q00 sits under Q00-Q07 Congenital malformations of the nervous system, within Chapter 17: Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99).
What coding notes apply to Q00?
ICD-10-CA lists Excludes notes for Q00, including those from the headings it sits under. They are listed on this page with where each one comes from.
Which ICD-10-CA release does this page use?
It uses CIHI’s FY 2026–2027 release, in effect from Apr 1, 2026 to Mar 31, 2027. It is a reference: confirm the code against the current list and the payer’s rules before you submit it.