K00.5 ICD-10-CA code: Hereditary disturbances in tooth structure, not elsewhere classified
K00.5 is the ICD-10-CA code for “Hereditary disturbances in tooth structure, not elsewhere classified” in CIHI’s FY 2026–2027 release, in effect from Apr 1, 2026.
Official description
K00.5Hereditary disturbances in tooth structure, not elsewhere classified
Short description: Hereditary disturb tooth structure NEC
ICD-10-CA · Canada · Also written K005
Index terms
Entries in CIHI’s alphabetical index that lead to K00.5. Searching the index by the condition the note names is how coders reach this code.
- Shell teeth
- Dysplasia, dentinal
- Amelogenesis imperfecta
- Odontogenesis imperfecta
- Dentinogenesis imperfecta
- Disturbance, tooth, structure, hereditary NEC
Notes for K00.5
As CIHI prints them, with any note K00.5 takes from the headings above it.
Includes
- Amelogenesis imperfectaDentinal dysplasiaDentinogenesis imperfectaOdontogenesis imperfectaShell teeth
Excludes
Conditions classified elsewhere.
- Embedded and impacted teeth (K01.-)From K00 Disorders of tooth development and eruption
- Certain:• conditions originating in the perinatal period (P00-P96)• infectious and parasitic diseases (A00-B99)complications of pregnancy, childbirth and the puerperium (O00-O99)congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)endocrine, nutritional and metabolic diseases (E00-E90)injury, poisoning and certain other consequences of external causes (S00-T98)neoplasms (C00-D48)symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R99)From Chapter 11: Diseases of the digestive system (K00-K93)
Where K00.5 sits
- 1ChapterChapter 11: Diseases of the digestive system (K00-K93)
- 2Block K00-K14Diseases of oral cavity, salivary glands and jaws
- 3Category K00Disorders of tooth development and eruption
- 4Valid code K00.5Hereditary disturbances in tooth structure, not elsewhere classified
Source and release
- Data release
- ICD-10-CA · FY 2026–2027
- Effective date
- Apr 1, 2026
- Publisher
- CIHI
This page is built from the ICD-10-CA catalog that Vero Codes reads when it suggests codes: Canadian Institute for Health Information’s FY 2026–2027 release, imported from the publisher’s file and checked against it. The description, notes and structured data come from the same record.
Frequently asked questions
What does ICD-10-CA code K00.5 mean?
K00.5 is the ICD-10-CA code for “Hereditary disturbances in tooth structure, not elsewhere classified” in CIHI’s ICD-10-CA FY 2026–2027 release.
Where is K00.5 in ICD-10-CA?
K00.5 sits under K00 Disorders of tooth development and eruption, within K00-K14 Diseases of oral cavity, salivary glands and jaws, within Chapter 11: Diseases of the digestive system (K00-K93).
What coding notes apply to K00.5?
ICD-10-CA lists Includes, Excludes notes for K00.5, including those from the headings it sits under. They are listed on this page with where each one comes from.
Which ICD-10-CA release does this page use?
It uses CIHI’s FY 2026–2027 release, in effect from Apr 1, 2026 to Mar 31, 2027. It is a reference: confirm the code against the current list and the payer’s rules before you submit it.