J99.1 ICD-10-CA code: Respiratory disorders in other diffuse connective tissue disorders

J99.1 is the ICD-10-CA code for “Respiratory disorders in other diffuse connective tissue disorders” in CIHI’s FY 2026–2027 release, in effect from Apr 1, 2026.

Official description

J99.1

Respiratory disorders in other diffuse connective tissue disorders

Short description: Resp disrd in oth diff con tissue disrd

ICD-10-CA · Canada · Also written J991

Notes for J99.1

As CIHI prints them, with any note J99.1 takes from the headings above it.

Includes

  • Respiratory disorders in:• dermatomyositis (M33.0-M33.1†)• granulomatosis with polyangiitis (M31.3†)• polymyositis (M33.2†)• sicca syndrome [Sjögren] (M35.0†)• systemic:• lupus erythematosus (M32.1†)• sclerosis (M34.8†)• Wegener granulomatosis (M31.3†)

Excludes

Conditions classified elsewhere.

  • Certain:• conditions originating in the perinatal period (P00-P96)• infectious and parasitic diseases (A00-B99)complications of pregnancy, childbirth and the puerperium (O00-O99)congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)endocrine, nutritional and metabolic diseases (E00-E90)injury, poisoning and certain other consequences of external causes (S00-T98)neoplasms (C00-D48)symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R99)From Chapter 10: Diseases of the respiratory system (J00-J99)

Note

  • When a respiratory condition is described as occurring in more than one site and is not specifically indexed, it should be classified to the lower anatomic site (e.g., tracheobronchitis to bronchitis in J40).From Chapter 10: Diseases of the respiratory system (J00-J99)

Where J99.1 sits

  1. 1ChapterChapter 10: Diseases of the respiratory system (J00-J99)
  2. 2Block J95-J99Other diseases of the respiratory system
  3. 3Category J99Respiratory disorders in diseases classified elsewhere
  4. 4Valid code J99.1Respiratory disorders in other diffuse connective tissue disorders

Source and release

Data release
ICD-10-CA · FY 2026–2027
Effective date
Apr 1, 2026
Publisher
CIHI

This page is built from the ICD-10-CA catalog that Vero Codes reads when it suggests codes: Canadian Institute for Health Information’s FY 2026–2027 release, imported from the publisher’s file and checked against it. The description, notes and structured data come from the same record.

Frequently asked questions

What does ICD-10-CA code J99.1 mean?

J99.1 is the ICD-10-CA code for “Respiratory disorders in other diffuse connective tissue disorders” in CIHI’s ICD-10-CA FY 2026–2027 release.

Where is J99.1 in ICD-10-CA?

J99.1 sits under J99 Respiratory disorders in diseases classified elsewhere, within J95-J99 Other diseases of the respiratory system, within Chapter 10: Diseases of the respiratory system (J00-J99).

What coding notes apply to J99.1?

ICD-10-CA lists Includes, Note, Excludes notes for J99.1, including those from the headings it sits under. They are listed on this page with where each one comes from.

Which ICD-10-CA release does this page use?

It uses CIHI’s FY 2026–2027 release, in effect from Apr 1, 2026 to Mar 31, 2027. It is a reference: confirm the code against the current list and the payer’s rules before you submit it.