I01 ICD-10-CA category: Rheumatic fever with heart involvement

I01 isn’t a code on its own. Choose one of the 5 codes beneath it, the one the documentation supports.

Official description

I01

Rheumatic fever with heart involvement

ICD-10-CA · Canada

Codes in I01

I01 isn’t a code on its own. Open the code that matches what the note documents.

Notes for I01

As CIHI prints them, with any note I01 takes from the headings above it.

Excludes

Conditions classified elsewhere.

  • Chronic diseases of rheumatic origin (I05-I09) unless rheumatic fever is also present or there is evidence of recrudescence or activity of the rheumatic process.
  • Certain:• conditions originating in the perinatal period (P00-P96)• infectious and parasitic diseases (A00-B99)complications of pregnancy, childbirth and the puerperium (O00-O99)congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)endocrine, nutritional and metabolic diseases (E00-E90)injury, poisoning and certain other consequences of external causes (S00-T98)neoplasms (C00-D48)symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R99)systemic connective tissue disorders (M30-M36)transient cerebral ischaemic attacks and related syndromes (G45.-)From Chapter 9: Diseases of the circulatory system (I00-I99)

Where I01 sits

  1. 1ChapterChapter 9: Diseases of the circulatory system (I00-I99)
  2. 2Block I00-I02Acute rheumatic fever
  3. 3Category I01Rheumatic fever with heart involvement

Source and release

Data release
ICD-10-CA · FY 2026–2027
Effective date
Apr 1, 2026
Publisher
CIHI

This page is built from the ICD-10-CA catalog that Vero Codes reads when it suggests codes: Canadian Institute for Health Information’s FY 2026–2027 release, imported from the publisher’s file and checked against it. The description, notes and structured data come from the same record.

Frequently asked questions

Is I01 a valid ICD-10-CA code?

No. I01 (Rheumatic fever with heart involvement) is a category heading in CIHI’s ICD-10-CA FY 2026–2027 release. It holds 5 codes; record the one the documentation supports.

Where is I01 in ICD-10-CA?

I01 sits under I00-I02 Acute rheumatic fever, within Chapter 9: Diseases of the circulatory system (I00-I99).

What coding notes apply to I01?

ICD-10-CA lists Excludes notes for I01, including those from the headings it sits under. They are listed on this page with where each one comes from.

Which ICD-10-CA release does this page use?

It uses CIHI’s FY 2026–2027 release, in effect from Apr 1, 2026 to Mar 31, 2027. It is a reference: confirm the code against the current list and the payer’s rules before you submit it.