G11.3 ICD-10-CA code: Cerebellar ataxia with defective DNA repair
G11.3 is the ICD-10-CA code for “Cerebellar ataxia with defective DNA repair” in CIHI’s FY 2026–2027 release, in effect from Apr 1, 2026.
Official description
G11.3Cerebellar ataxia with defective DNA repair
Short description: Cerebellar ataxia w defective DNA repair
ICD-10-CA · Canada · Also written G113
Index terms
Entries in CIHI’s alphabetical index that lead to G11.3. Searching the index by the condition the note names is how coders reach this code.
- Louis Bar syndrome
- Syndrome, ataxia telangiectasia
- Ataxia telangiectasia (Louis Bar)
- Ataxia, ataxy, ataxic, telangiectasia (Louis Bar)
- Ataxia, ataxy, ataxic, cerebellar, with defective DNA repair
- Telangiectasia, telangiectasis (verrucous), ataxic (cerebellar) (Louis-Bar)
Notes for G11.3
As CIHI prints them, with any note G11.3 takes from the headings above it.
Includes
- Ataxia telangiectasia [Louis-Bar]
Excludes
Conditions classified elsewhere.
- Cockayne's syndrome (Q87.1)xeroderma pigmentosum (Q82.1)
- Cerebral palsy (G80.-)hereditary and idiopathic neuropathy (G60.-)metabolic disorders (E70-E90)From G11 Hereditary ataxia
- Certain:• conditions originating in the perinatal period (P00-P96)• infectious and parasitic diseases (A00-B99)complications of pregnancy, childbirth and the puerperium (O00-O99)congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)endocrine, nutritional and metabolic diseases (E00-E90)injury, poisoning and certain other consequences of external causes (S00-T98)neoplasms (C00-D48)symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R99)From Chapter 6: Diseases of the nervous system (G00-G99)
Where G11.3 sits
- 1ChapterChapter 6: Diseases of the nervous system (G00-G99)
- 2Block G10-G14Systemic atrophies primarily affecting the central nervous system
- 3Category G11Hereditary ataxia
- 4Valid code G11.3Cerebellar ataxia with defective DNA repair
Source and release
- Data release
- ICD-10-CA · FY 2026–2027
- Effective date
- Apr 1, 2026
- Publisher
- CIHI
This page is built from the ICD-10-CA catalog that Vero Codes reads when it suggests codes: Canadian Institute for Health Information’s FY 2026–2027 release, imported from the publisher’s file and checked against it. The description, notes and structured data come from the same record.
Frequently asked questions
What does ICD-10-CA code G11.3 mean?
G11.3 is the ICD-10-CA code for “Cerebellar ataxia with defective DNA repair” in CIHI’s ICD-10-CA FY 2026–2027 release.
Where is G11.3 in ICD-10-CA?
G11.3 sits under G11 Hereditary ataxia, within G10-G14 Systemic atrophies primarily affecting the central nervous system, within Chapter 6: Diseases of the nervous system (G00-G99).
What coding notes apply to G11.3?
ICD-10-CA lists Includes, Excludes notes for G11.3, including those from the headings it sits under. They are listed on this page with where each one comes from.
Which ICD-10-CA release does this page use?
It uses CIHI’s FY 2026–2027 release, in effect from Apr 1, 2026 to Mar 31, 2027. It is a reference: confirm the code against the current list and the payer’s rules before you submit it.