E78.0 ICD-10-CA code: Pure hypercholesterolaemia
E78.0 is the ICD-10-CA code for “Pure hypercholesterolaemia” in CIHI’s FY 2026–2027 release, in effect from Apr 1, 2026.
Official description
E78.0Pure hypercholesterolaemia
ICD-10-CA · Canada · Also written E780
Index terms
Entries in CIHI’s alphabetical index that lead to E78.0. Searching the index by the condition the note names is how coders reach this code.
- Hyperbetalipoproteinemia (familial)
- Hyperlipemia, hyperlipidemia, group, A
- Hyperlipoproteinemia, Fredrickson's type, IIa
- Frederickson's hyperlipoproteinemia, type, IIA
- Low density lipoprotein type (LDL) hyperlipoproteinemia
- Hyperlipoproteinemia, low density lipoprotein type (LDL)
- Cholesterolemia (essential) (familial) (hereditary) (pure)
- Hypercholesterolemia (essential) (familial) (hereditary) (primary) (pure)
- Xanthoma(s), xanthomatosis (primary) (familial) (hereditary), hypercholesterolemic
Notes for E78.0
As CIHI prints them, with any note E78.0 takes from the headings above it.
Includes
- Familial hypercholesterolaemiaFredrickson's hyperlipoproteinaemia, type IIaHyperbetalipoproteinaemiaHyperlipidaemia, group ALow-density-lipoprotein-type [LDL] hyperlipoproteinaemia
Excludes
Conditions classified elsewhere.
- Sphingolipidosis (E75.0-E75.3)From E78 Disorders of lipoprotein metabolism and other lipidaemias
- 5-alpha -reductase deficiency (E29.1)androgen resistance syndrome (E34.5)congenital adrenal hyperplasia (E25.0)Ehlers-Danlos syndrome (Q79.6)haemolytic anaemias due to enzyme disorders (D55.-)Marfan's syndrome (Q87.4)From E70-E90 Metabolic disorders
- Complications of pregnancy, childbirth and the puerperium (O00-O99)symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R99)transitory endocrine and metabolic disorders specific to fetus and newborn (P70-P74)From Chapter 4: Endocrine, nutritional and metabolic diseases (E00-E90)
Note
- All neoplasms, whether functionally active or not, are classified in Chapter II. Appropriate codes in this chapter (i.e. E05.8)(E07.0) (E16-E31)(E34.-) may be used, if desired, as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.From Chapter 4: Endocrine, nutritional and metabolic diseases (E00-E90)
Where E78.0 sits
- 1ChapterChapter 4: Endocrine, nutritional and metabolic diseases (E00-E90)
- 2Block E70-E90Metabolic disorders
- 3Category E78Disorders of lipoprotein metabolism and other lipidaemias
- 4Valid code E78.0Pure hypercholesterolaemia
Source and release
- Data release
- ICD-10-CA · FY 2026–2027
- Effective date
- Apr 1, 2026
- Publisher
- CIHI
This page is built from the ICD-10-CA catalog that Vero Codes reads when it suggests codes: Canadian Institute for Health Information’s FY 2026–2027 release, imported from the publisher’s file and checked against it. The description, notes and structured data come from the same record.
Frequently asked questions
What does ICD-10-CA code E78.0 mean?
E78.0 is the ICD-10-CA code for “Pure hypercholesterolaemia” in CIHI’s ICD-10-CA FY 2026–2027 release.
Where is E78.0 in ICD-10-CA?
E78.0 sits under E78 Disorders of lipoprotein metabolism and other lipidaemias, within E70-E90 Metabolic disorders, within Chapter 4: Endocrine, nutritional and metabolic diseases (E00-E90).
What coding notes apply to E78.0?
ICD-10-CA lists Includes, Excludes, Note notes for E78.0, including those from the headings it sits under. They are listed on this page with where each one comes from.
Which ICD-10-CA release does this page use?
It uses CIHI’s FY 2026–2027 release, in effect from Apr 1, 2026 to Mar 31, 2027. It is a reference: confirm the code against the current list and the payer’s rules before you submit it.