E76 ICD-10-CA category: Disorders of glycosaminoglycan metabolism
E76 isn’t a code on its own. Choose one of the 6 codes beneath it, the one the documentation supports.
Official description
E76Disorders of glycosaminoglycan metabolism
ICD-10-CA · Canada
Codes in E76
E76 isn’t a code on its own. Open the code that matches what the note documents.
Notes for E76
As CIHI prints them, with any note E76 takes from the headings above it.
Excludes
Conditions classified elsewhere.
- 5-alpha -reductase deficiency (E29.1)androgen resistance syndrome (E34.5)congenital adrenal hyperplasia (E25.0)Ehlers-Danlos syndrome (Q79.6)haemolytic anaemias due to enzyme disorders (D55.-)Marfan's syndrome (Q87.4)From E70-E90 Metabolic disorders
- Complications of pregnancy, childbirth and the puerperium (O00-O99)symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R99)transitory endocrine and metabolic disorders specific to fetus and newborn (P70-P74)From Chapter 4: Endocrine, nutritional and metabolic diseases (E00-E90)
Note
- All neoplasms, whether functionally active or not, are classified in Chapter II. Appropriate codes in this chapter (i.e. E05.8)(E07.0) (E16-E31)(E34.-) may be used, if desired, as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.From Chapter 4: Endocrine, nutritional and metabolic diseases (E00-E90)
Where E76 sits
- 1ChapterChapter 4: Endocrine, nutritional and metabolic diseases (E00-E90)
- 2Block E70-E90Metabolic disorders
- 3Category E76Disorders of glycosaminoglycan metabolism
Source and release
- Data release
- ICD-10-CA · FY 2026–2027
- Effective date
- Apr 1, 2026
- Publisher
- CIHI
This page is built from the ICD-10-CA catalog that Vero Codes reads when it suggests codes: Canadian Institute for Health Information’s FY 2026–2027 release, imported from the publisher’s file and checked against it. The description, notes and structured data come from the same record.
Frequently asked questions
Is E76 a valid ICD-10-CA code?
No. E76 (Disorders of glycosaminoglycan metabolism) is a category heading in CIHI’s ICD-10-CA FY 2026–2027 release. It holds 6 codes; record the one the documentation supports.
Where is E76 in ICD-10-CA?
E76 sits under E70-E90 Metabolic disorders, within Chapter 4: Endocrine, nutritional and metabolic diseases (E00-E90).
What coding notes apply to E76?
ICD-10-CA lists Excludes, Note notes for E76, including those from the headings it sits under. They are listed on this page with where each one comes from.
Which ICD-10-CA release does this page use?
It uses CIHI’s FY 2026–2027 release, in effect from Apr 1, 2026 to Mar 31, 2027. It is a reference: confirm the code against the current list and the payer’s rules before you submit it.
Codes beside E76
View E70-E90E70Disorders of aromatic amino-acid metabolismE71Disorders of branched-chain amino-acid metabolism and fatty-acid metabolismE72Other disorders of amino-acid metabolismE73Lactose intoleranceE74Other disorders of carbohydrate metabolismE75Disorders of sphingolipid metabolism and other lipid storage disordersE77Disorders of glycoprotein metabolismE78Disorders of lipoprotein metabolism and other lipidaemiasE79Disorders of purine and pyrimidine metabolismE80Disorders of porphyrin and bilirubin metabolismE83Disorders of mineral metabolismE84Cystic fibrosisE85AmyloidosisE86Volume depletionE87Other disorders of fluid, electrolyte and acid-base balanceE88Other metabolic disordersE89Postprocedural endocrine and metabolic disorders, not elsewhere classifiedE90Nutritional and metabolic disorders in diseases classified elsewhere