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D82.1 ICD-10-CA code: Di George's syndrome

D82.1 is the ICD-10-CA code for “Di George's syndrome” in CIHI’s FY 2026–2027 release, in effect from Apr 1, 2026.

Official description

D82.1

Di George's syndrome

ICD-10-CA · Canada · Also written D821

Index terms

Entries in CIHI’s alphabetical index that lead to D82.1. Searching the index by the condition the note names is how coders reach this code.

  • Alymphoplasia, thymic
  • Pharyngeal pouch syndrome
  • Syndrome, pharyngeal pouch
  • Aplasia, parathyroid thymic
  • Aplasia, thymic, with immunodeficiency
  • Dysplasia, thymic, with immunodeficiency
  • Alymphocytosis, thymic (with immunodeficiency)
  • Hypoplasia, hypoplastic, thymic, with immunodeficiency
  • Hypoplasia, hypoplastic, thymus (gland), with immunodeficiency

Notes for D82.1

As CIHI prints them, with any note D82.1 takes from the headings above it.

Includes

Excludes

Conditions classified elsewhere.

  • Ataxia telangiectasia [Louis-Bar] (G11.3)From D82 Immunodeficiency associated with other major defects
  • Autoimmune disease (systemic) NOS (M35.9)functional disorders of polymorphonuclear neutrophils (D71)human immunodeficiency virus [HIV] disease (B24)human immunodeficiency virus [HIV] disease complicating pregnancy, childbirth and the puerperium (O98.7-)From D80-D89 Certain disorders involving the immune mechanism
  • Autoimmune disease (systemic) NOS (M35.9)certain conditions originating in the perinatal period (P00-P96)complications of pregnancy, childbirth and the puerperium (O00-O99)congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)endocrine, nutritional and metabolic diseases (E00-E90)human immunodeficiency virus [HIV] disease (B24)injury, poisoning and certain other consequences of external causes (S00-T98)neoplasms (C00-D48)symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R99)From Chapter 3: Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)

Where D82.1 sits

  1. 1ChapterChapter 3: Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
  2. 2Block D80-D89Certain disorders involving the immune mechanism
  3. 3Category D82Immunodeficiency associated with other major defects
  4. 4Valid code D82.1Di George's syndrome

Source and release

Data release
ICD-10-CA · FY 2026–2027
Effective date
Apr 1, 2026
Publisher
CIHI

This page is built from the ICD-10-CA catalog that Vero Codes reads when it suggests codes: Canadian Institute for Health Information’s FY 2026–2027 release, imported from the publisher’s file and checked against it. The description, notes and structured data come from the same record.

See D82.1 in the CIHI source

Frequently asked questions

What does ICD-10-CA code D82.1 mean?

D82.1 is the ICD-10-CA code for “Di George's syndrome” in CIHI’s ICD-10-CA FY 2026–2027 release.

Where is D82.1 in ICD-10-CA?

D82.1 sits under D82 Immunodeficiency associated with other major defects, within D80-D89 Certain disorders involving the immune mechanism, within Chapter 3: Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89).

What coding notes apply to D82.1?

ICD-10-CA lists Includes, Excludes notes for D82.1, including those from the headings it sits under. They are listed on this page with where each one comes from.

Which ICD-10-CA release does this page use?

It uses CIHI’s FY 2026–2027 release, in effect from Apr 1, 2026 to Mar 31, 2027. It is a reference: confirm the code against the current list and the payer’s rules before you submit it.

Codes beside D82.1

D82.0Wiskott-Aldrich syndromeD82.2Immunodeficiency with short-limbed statureD82.3Immunodeficiency following hereditary defective response to Epstein-Barr virusD82.4Hyperimmunoglobulin E [IgE] syndromeD82.8Immunodeficiency associated with other specified major defectsD82.9Immunodeficiency associated with major defect, unspecified