D76.3 ICD-10-CA code: Other histiocytosis syndromes
D76.3 is the ICD-10-CA code for “Other histiocytosis syndromes” in CIHI’s FY 2026–2027 release, in effect from Apr 1, 2026.
Official description
D76.3Other histiocytosis syndromes
ICD-10-CA · Canada · Also written D763
Index terms
Entries in CIHI’s alphabetical index that lead to D76.3. Searching the index by the condition the note names is how coders reach this code.
- Histiocytosis
- Xanthogranuloma
- Histiocytosis, syndrome NEC
- Syndrome, histiocytosis NEC
- Granuloma, reticulohistiocytic
- Reticulohistiocytoma (giant cell)
- Histiocytosis, sinus, with massive lymphadenopathy
Notes for D76.3
As CIHI prints them, with any note D76.3 takes from the headings above it.
Includes
- Reticulohistiocytoma (giant-cell)Sinus histiocytosis with massive lymphadenopathyXanthogranuloma
Excludes
Conditions classified elsewhere.
- (Abt-)Letterer-Siwe disease (C96.0)eosinophilic granuloma (C96.6)Hand-Schüller-Christian disease (C96.5)histiocytic sarcoma (C96.8)histiocytosis X, multifocal (C96.5)histiocytosis X, unifocal (C96.6)Langerhans-cell histiocytosis, multifocal (C96.5)Langerhans-cell histiocytosis, unifocal (C96.6)malignant histiocytosis (C96.8)reticuloendotheliosis:• leukaemic (C91.4)• nonlipid (C96.0)reticulosis:• histiocytic medullary (C96.8)• lipomelanotic (I89.8)• malignant NOS (C86.0)From D76 Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue
- Autoimmune disease (systemic) NOS (M35.9)certain conditions originating in the perinatal period (P00-P96)complications of pregnancy, childbirth and the puerperium (O00-O99)congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)endocrine, nutritional and metabolic diseases (E00-E90)human immunodeficiency virus [HIV] disease (B24)injury, poisoning and certain other consequences of external causes (S00-T98)neoplasms (C00-D48)symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R99)From Chapter 3: Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
Where D76.3 sits
- 1ChapterChapter 3: Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
- 2Block D70-D77Other diseases of blood and blood-forming organs
- 3Category D76Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue
- 4Valid code D76.3Other histiocytosis syndromes
Source and release
- Data release
- ICD-10-CA · FY 2026–2027
- Effective date
- Apr 1, 2026
- Publisher
- CIHI
This page is built from the ICD-10-CA catalog that Vero Codes reads when it suggests codes: Canadian Institute for Health Information’s FY 2026–2027 release, imported from the publisher’s file and checked against it. The description, notes and structured data come from the same record.
Frequently asked questions
What does ICD-10-CA code D76.3 mean?
D76.3 is the ICD-10-CA code for “Other histiocytosis syndromes” in CIHI’s ICD-10-CA FY 2026–2027 release.
Where is D76.3 in ICD-10-CA?
D76.3 sits under D76 Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue, within D70-D77 Other diseases of blood and blood-forming organs, within Chapter 3: Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89).
What coding notes apply to D76.3?
ICD-10-CA lists Includes, Excludes notes for D76.3, including those from the headings it sits under. They are listed on this page with where each one comes from.
Which ICD-10-CA release does this page use?
It uses CIHI’s FY 2026–2027 release, in effect from Apr 1, 2026 to Mar 31, 2027. It is a reference: confirm the code against the current list and the payer’s rules before you submit it.