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U.S. ICD-10-CM · FY 2027

Q87.A ICD-10-CM Code: Loeys-Dietz syndrome

A clear reference for the official code description, hierarchy, and related coding information from the FY 2027 U.S. release.

Code definition

Official description

Q87.A

Loeys-Dietz syndrome

ICD-10-CM diagnosis code · United States clinical modification

Classification

Where Q87.A sits

  1. 1

    Chapter 17

    Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)

  2. 2

    Section

    Other congenital malformations (Q80-Q89)

  3. 3

    Category Q87

    Other specified congenital malformation syndromes affecting multiple systems

  4. 4

    Code Q87.A

    Loeys-Dietz syndrome

Documentation details

Notes for this code

Inclusion terms

No inclusion terms are listed for Q87.A.

Code first

No “code first” instruction is listed for Q87.A.

Use additional code

No “use additional code” instruction is listed for Q87.A.

Excludes1

Conditions that should not be reported together with this code.

  • arterial tortuosity syndrome (Q87.82)
  • Ehlers-Danlos syndrome (Q79.6)
  • Marfan syndrome (Q87.40-Q87.43)
  • other systemic involvement of connective tissue (M35)

Excludes2

Conditions not included here that may be reported separately when present.

No Excludes2 note is listed for Q87.A.

Transparency

Source and release

Data release

U.S. ICD-10-CM · FY 2027

Effective date

Oct 1, 2026

This reference is generated from Vero’s ICD-10-CM description, hierarchy, and code-note dataset. The visible content and structured data share that source.

Review the CDC/NCHS ICD-10-CM source

Code-specific guidance

Frequently asked questions

What does ICD-10-CM code Q87.A mean?

Q87.A is the FY 2027 U.S. ICD-10-CM code for “Loeys-Dietz syndrome.”

Is Q87.A a billable or specific ICD-10-CM code?

Yes. In the FY 2027 reference data used on this page, Q87.A has no child codes and is presented as a billable/specific code. Always confirm the active code set and payer requirements before use.

Where is Q87.A located in ICD-10-CM?

Q87.A is listed in Chapter 17, Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1), within Other congenital malformations (Q80-Q89) (Q80–Q89), under category Q87, Other specified congenital malformation syndromes affecting multiple systems.

What coding notes are listed for Q87.A?

No inclusion terms are listed for Q87.A in this reference record. No code-first instruction is listed. Excludes1 notes: arterial tortuosity syndrome (Q87.82); Ehlers-Danlos syndrome (Q79.6); Marfan syndrome (Q87.40-Q87.43); other systemic involvement of connective tissue (M35). No Excludes2 note is listed.

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