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U.S. ICD-10-CM · FY 2027

M04.3 ICD-10-CM Code: VEXAS syndrome

A clear reference for the official code description, hierarchy, and related coding information from the FY 2027 U.S. release.

Code definition

Official description

M04.3

VEXAS syndrome

ICD-10-CM diagnosis code · United States clinical modification

Classification

Where M04.3 sits

  1. 1

    Chapter 13

    Diseases of the musculoskeletal system and connective tissue (M00-M99)

  2. 2

    Section

    Autoinflammatory syndromes (M04)

  3. 3

    Category M04

    Autoinflammatory syndromes

  4. 4

    Code M04.3

    VEXAS syndrome

Documentation details

Notes for this code

Inclusion terms

  • Vacuoles, E1 ubiquitin-activating enzyme, X-linked, autoinflammatory, somatic syndrome

Code first

No “code first” instruction is listed for M04.3.

Use additional code

No “use additional code” instruction is listed for M04.3.

Excludes1

Conditions that should not be reported together with this code.

No Excludes1 note is listed for M04.3.

Excludes2

Conditions not included here that may be reported separately when present.

No Excludes2 note is listed for M04.3.

Transparency

Source and release

Data release

U.S. ICD-10-CM · FY 2027

Effective date

Oct 1, 2026

This reference is generated from Vero’s ICD-10-CM description, hierarchy, and code-note dataset. The visible content and structured data share that source.

Review the CDC/NCHS ICD-10-CM source

Code-specific guidance

Frequently asked questions

What does ICD-10-CM code M04.3 mean?

M04.3 is the FY 2027 U.S. ICD-10-CM code for “VEXAS syndrome.”

Is M04.3 a billable or specific ICD-10-CM code?

Yes. In the FY 2027 reference data used on this page, M04.3 has no child codes and is presented as a billable/specific code. Always confirm the active code set and payer requirements before use.

Where is M04.3 located in ICD-10-CM?

M04.3 is listed in Chapter 13, Diseases of the musculoskeletal system and connective tissue (M00-M99), within Autoinflammatory syndromes (M04) (M04–M04), under category M04, Autoinflammatory syndromes.

What coding notes are listed for M04.3?

Its listed inclusion terms are Vacuoles, E1 ubiquitin-activating enzyme, X-linked, autoinflammatory, somatic syndrome. No code-first instruction is listed. No Excludes1 note is listed. No Excludes2 note is listed.

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