J84.81 ICD-10-CM Code: Lymphangioleiomyomatosis
A clear reference for the official code description, hierarchy, and related coding information from the FY 2027 U.S. release.
Official description
J84.81Lymphangioleiomyomatosis
ICD-10-CM diagnosis code · United States clinical modification
Where J84.81 sits
- 1
Chapter 10
Diseases of the respiratory system (J00-J99)
- 2
Section
Other respiratory diseases principally affecting the interstitium (J80-J84)
- 3
Category J84
Other interstitial pulmonary diseases
- 4
Subcategory J84.8
Other specified interstitial pulmonary diseases
- 5
Code J84.81
Lymphangioleiomyomatosis
Notes for this code
Inclusion terms
- Lymphangiomyomatosis
Code first
No “code first” instruction is listed for J84.81.
Use additional code
No “use additional code” instruction is listed for J84.81.
Excludes1
Conditions that should not be reported together with this code.
No Excludes1 note is listed for J84.81.
Excludes2
Conditions not included here that may be reported separately when present.
No Excludes2 note is listed for J84.81.
Source and release
- Data release
- U.S. ICD-10-CM · FY 2027
- Effective date
- Oct 1, 2026
- Publisher
- Vero Scribe Inc.
This reference is generated from Vero’s ICD-10-CM description, hierarchy, and code-note dataset. The visible content and structured data share that source.
Frequently asked questions
What does ICD-10-CM code J84.81 mean?
J84.81 is the FY 2027 U.S. ICD-10-CM code for “Lymphangioleiomyomatosis.”
Is J84.81 a billable or specific ICD-10-CM code?
Yes. In the FY 2027 reference data used on this page, J84.81 has no child codes and is presented as a billable/specific code. Always confirm the active code set and payer requirements before use.
Where is J84.81 located in ICD-10-CM?
J84.81 is listed in Chapter 10, Diseases of the respiratory system (J00-J99), within Other respiratory diseases principally affecting the interstitium (J80-J84) (J80–J84), under category J84, Other interstitial pulmonary diseases and subcategory J84.8, Other specified interstitial pulmonary diseases.
What coding notes are listed for J84.81?
Its listed inclusion terms are Lymphangiomyomatosis. No code-first instruction is listed. No Excludes1 note is listed. No Excludes2 note is listed.