G71.3 ICD-10-CM Code: Mitochondrial myopathy, not elsewhere classified
G71.3 is the billable ICD-10-CM code for “Mitochondrial myopathy, not elsewhere classified” in the FY 2027 U.S. code set, effective Oct 1, 2026.
Official description
G71.3Mitochondrial myopathy, not elsewhere classified
ICD-10-CM diagnosis code · United States clinical modification
Where G71.3 sits
- 1
Chapter 6
Diseases of the nervous system (G00-G99)
- 2
Section
Diseases of myoneural junction and muscle (G70-G73)
- 3
Category G71
Primary disorders of muscles
- 4
Code G71.3
Mitochondrial myopathy, not elsewhere classified
Notes for this code
Inclusion terms
No inclusion terms are listed for G71.3.
Code first
No “code first” instruction is listed for G71.3.
Use additional code
No “use additional code” instruction is listed for G71.3.
Excludes1
Conditions that should not be reported together with this code.
- Kearns-Sayre syndrome (H49.81)
- Leber's disease (H47.21)
- Leigh's encephalopathy (G31.82)
- mitochondrial metabolism disorders (E88.4.-)
- Reye's syndrome (G93.7)
Excludes2
Conditions not included here that may be reported separately when present.
No Excludes2 note is listed for G71.3.
Source and release
- Data release
- U.S. ICD-10-CM · FY 2027
- Effective date
- Oct 1, 2026
- Publisher
- Vero Scribe Inc.
This reference is generated from Vero’s ICD-10-CM description, hierarchy, and code-note dataset. The visible content and structured data share that source.
Frequently asked questions
What does ICD-10-CM code G71.3 mean?
G71.3 is the FY 2027 U.S. ICD-10-CM code for “Mitochondrial myopathy, not elsewhere classified.”
Is G71.3 a billable or specific ICD-10-CM code?
Yes. In the FY 2027 reference data used on this page, G71.3 has no child codes and is presented as a billable/specific code. Always confirm the active code set and payer requirements before use.
Where is G71.3 located in ICD-10-CM?
G71.3 is listed in Chapter 6, Diseases of the nervous system (G00-G99), within Diseases of myoneural junction and muscle (G70-G73) (G70–G73), under category G71, Primary disorders of muscles.
What coding notes are listed for G71.3?
No inclusion terms are listed for G71.3 in this reference record. No code-first instruction is listed. Excludes1 notes: Kearns-Sayre syndrome (H49.81); Leber's disease (H47.21); Leigh's encephalopathy (G31.82); mitochondrial metabolism disorders (E88.4.-); Reye's syndrome (G93.7). No Excludes2 note is listed.