G40.42 ICD-10-CM Code: Cyclin-Dependent Kinase-Like 5 Deficiency Disorder
A clear reference for the official code description, hierarchy, and related coding information from the FY 2027 U.S. release.
Official description
G40.42Cyclin-Dependent Kinase-Like 5 Deficiency Disorder
ICD-10-CM diagnosis code · United States clinical modification
Where G40.42 sits
- 1
Chapter 6
Diseases of the nervous system (G00-G99)
- 2
Section
Episodic and paroxysmal disorders (G40-G47)
- 3
Category G40
Epilepsy and recurrent seizures
- 4
Subcategory G40.4
Other generalized epilepsy and epileptic syndromes
- 5
Code G40.42
Cyclin-Dependent Kinase-Like 5 Deficiency Disorder
Notes for this code
Inclusion terms
- CDKL5
Code first
No “code first” instruction is listed for G40.42.
Use additional code
- code, if known, to identify associated manifestations, such as:
- cortical blindness (H47.61-)
- global developmental delay (F88)
Excludes1
Conditions that should not be reported together with this code.
No Excludes1 note is listed for G40.42.
Excludes2
Conditions not included here that may be reported separately when present.
No Excludes2 note is listed for G40.42.
Source and release
- Data release
- U.S. ICD-10-CM · FY 2027
- Effective date
- Oct 1, 2026
- Publisher
- Vero Scribe Inc.
This reference is generated from Vero’s ICD-10-CM description, hierarchy, and code-note dataset. The visible content and structured data share that source.
Frequently asked questions
What does ICD-10-CM code G40.42 mean?
G40.42 is the FY 2027 U.S. ICD-10-CM code for “Cyclin-Dependent Kinase-Like 5 Deficiency Disorder.”
Is G40.42 a billable or specific ICD-10-CM code?
Yes. In the FY 2027 reference data used on this page, G40.42 has no child codes and is presented as a billable/specific code. Always confirm the active code set and payer requirements before use.
Where is G40.42 located in ICD-10-CM?
G40.42 is listed in Chapter 6, Diseases of the nervous system (G00-G99), within Episodic and paroxysmal disorders (G40-G47) (G40–G47), under category G40, Epilepsy and recurrent seizures and subcategory G40.4, Other generalized epilepsy and epileptic syndromes.
What coding notes are listed for G40.42?
Its listed inclusion terms are CDKL5. No code-first instruction is listed. Additional-code instructions: code, if known, to identify associated manifestations, such as:; cortical blindness (H47.61-); global developmental delay (F88). No Excludes1 note is listed. No Excludes2 note is listed.