U.S. ICD-10-CM · FY 2027

G11 ICD-10-CM Code: Hereditary ataxia

A clear reference for the official code description, hierarchy, and related coding information from the FY 2027 U.S. release.

Code definition

Official description

G11

Hereditary ataxia

ICD-10-CM diagnosis code · United States clinical modification

Classification

Where G11 sits

  1. 1

    Chapter 6

    Diseases of the nervous system (G00-G99)

  2. 2

    Section

    Systemic atrophies primarily affecting the central nervous system (G10-G14)

  3. 3

    Category G11

    Hereditary ataxia

  4. 4

    Code G11

    Hereditary ataxia

More specific choices

Codes under G11

G11 is a non-billable category. Choose the child code that best matches the documented diagnosis.

G11.0

Congenital nonprogressive ataxia

G11.1

Early-onset cerebellar ataxia

G11.2

Late-onset cerebellar ataxia

G11.3

Cerebellar ataxia with defective DNA repair

G11.4

Hereditary spastic paraplegia

G11.5

Hypomyelination - hypogonadotropic hypogonadism - hypodontia

G11.6

Leukodystrophy with vanishing white matter disease

G11.8

Other hereditary ataxias

G11.9

Hereditary ataxia, unspecified

Documentation details

Notes for this code

Inclusion terms

No inclusion terms are listed for G11.

Code first

No “code first” instruction is listed for G11.

Use additional code

No “use additional code” instruction is listed for G11.

Excludes1

Conditions that should not be reported together with this code.

No Excludes1 note is listed for G11.

Excludes2

Conditions not included here that may be reported separately when present.

  • cerebral palsy (G80.-)
  • hereditary and idiopathic neuropathy (G60.-)
  • metabolic disorders (E70-E88)

Transparency

Source and release

Data release

U.S. ICD-10-CM · FY 2027

Effective date

Oct 1, 2026

Publisher

Vero Scribe Inc.

This reference is generated from Vero’s ICD-10-CM description, hierarchy, and code-note dataset. The visible content and structured data share that source.

Review the CDC/NCHS ICD-10-CM source

Code-specific guidance

Frequently asked questions

What does ICD-10-CM code G11 mean?

G11 is the FY 2027 U.S. ICD-10-CM code for “Hereditary ataxia.”

Is G11 a billable or specific ICD-10-CM code?

No. G11 has more specific child codes in the FY 2027 reference data. Select the code that matches the documentation and confirm the active code set and payer requirements.

Where is G11 located in ICD-10-CM?

G11 is listed in Chapter 6, Diseases of the nervous system (G00-G99), within Systemic atrophies primarily affecting the central nervous system (G10-G14) (G10–G14), under category G11, Hereditary ataxia.

What coding notes are listed for G11?

No inclusion terms are listed for G11 in this reference record. No code-first instruction is listed. No Excludes1 note is listed. Excludes2 notes: cerebral palsy (G80.-); hereditary and idiopathic neuropathy (G60.-); metabolic disorders (E70-E88).

Ready to transform your clinical documentation?

Join Vero and see how effortless documentation can be.

Try for free

  • No credit card required

  • Cancel anytime