E78.01 ICD-10-CM Code: Familial hypercholesterolemia
E78.01 isn’t billable on its own. Choose one of the 3 billable codes beneath it, the one the documentation supports.
Official description
E78.01Familial hypercholesterolemia
ICD-10-CM diagnosis code · United States clinical modification
Billable codes under E78.01
E78.01 can’t be reported on its own. Choose the code below that matches what the note documents.
Where E78.01 sits
- 1
Chapter 4
Endocrine, nutritional and metabolic diseases (E00-E89)
- 2
Section
Metabolic disorders (E70-E88)
- 3
Category E78
Disorders of lipoprotein metabolism and other lipidemias
- 4
Subcategory E78.0
Pure hypercholesterolemia
- 5
Code E78.01
Familial hypercholesterolemia
Notes for this code
Inclusion terms
No inclusion terms are listed for E78.01.
Code first
No “code first” instruction is listed for E78.01.
Use additional code
No “use additional code” instruction is listed for E78.01.
Excludes1
Conditions that should not be reported together with this code.
No Excludes1 note is listed for E78.01.
Excludes2
Conditions not included here that may be reported separately when present.
No Excludes2 note is listed for E78.01.
Source and release
- Data release
- U.S. ICD-10-CM · FY 2027
- Effective date
- Oct 1, 2026
- Publisher
- Vero Scribe Inc.
This reference is generated from Vero’s ICD-10-CM description, hierarchy, and code-note dataset. The visible content and structured data share that source.
Frequently asked questions
What does ICD-10-CM code E78.01 mean?
E78.01 is the FY 2027 U.S. ICD-10-CM code for “Familial hypercholesterolemia.”
Is E78.01 a billable or specific ICD-10-CM code?
No. E78.01 has 3 billable codes beneath it in the FY 2027 reference data. Select the code that matches the documentation and confirm the active code set and payer requirements.
Where is E78.01 located in ICD-10-CM?
E78.01 is listed in Chapter 4, Endocrine, nutritional and metabolic diseases (E00-E89), within Metabolic disorders (E70-E88) (E70–E88), under category E78, Disorders of lipoprotein metabolism and other lipidemias and subcategory E78.0, Pure hypercholesterolemia.
What coding notes are listed for E78.01?
No inclusion terms are listed for E78.01 in this reference record. No code-first instruction is listed. No Excludes1 note is listed. No Excludes2 note is listed.