E75.3 ICD-10-CM Code: Sphingolipidosis, unspecified

E75.3 is the billable ICD-10-CM code for “Sphingolipidosis, unspecified” in the FY 2027 U.S. code set, effective Oct 1, 2026.

Official description

E75.3

Sphingolipidosis, unspecified

ICD-10-CM diagnosis code · United States clinical modification

More specific than E75.3

E75.3 is an unspecified code, for when the note doesn’t say more. If it documents the type, cause, or site, one of these codes may fit better.

Where E75.3 sits

  1. 1

    Chapter 4

    Endocrine, nutritional and metabolic diseases (E00-E89)

  2. 2

    Section

    Metabolic disorders (E70-E88)

  3. 3

    Category E75

    Disorders of sphingolipid metabolism and other lipid storage disorders

  4. 4

    Code E75.3

    Sphingolipidosis, unspecified

Notes for this code

Inclusion terms

No inclusion terms are listed for E75.3.

Code first

No “code first” instruction is listed for E75.3.

Use additional code

No “use additional code” instruction is listed for E75.3.

Excludes1

Conditions that should not be reported together with this code.

No Excludes1 note is listed for E75.3.

Excludes2

Conditions not included here that may be reported separately when present.

No Excludes2 note is listed for E75.3.

Source and release

Data release
U.S. ICD-10-CM · FY 2027
Effective date
Oct 1, 2026

This reference is generated from Vero’s ICD-10-CM description, hierarchy, and code-note dataset. The visible content and structured data share that source.

Frequently asked questions

What does ICD-10-CM code E75.3 mean?

E75.3 is the FY 2027 U.S. ICD-10-CM code for “Sphingolipidosis, unspecified.”

Is E75.3 a billable or specific ICD-10-CM code?

Yes. In the FY 2027 reference data used on this page, E75.3 has no child codes and is presented as a billable/specific code. Always confirm the active code set and payer requirements before use.

Where is E75.3 located in ICD-10-CM?

E75.3 is listed in Chapter 4, Endocrine, nutritional and metabolic diseases (E00-E89), within Metabolic disorders (E70-E88) (E70–E88), under category E75, Disorders of sphingolipid metabolism and other lipid storage disorders.

What coding notes are listed for E75.3?

No inclusion terms are listed for E75.3 in this reference record. No code-first instruction is listed. No Excludes1 note is listed. No Excludes2 note is listed.