U.S. ICD-10-CM · FY 2027

E75.249 ICD-10-CM Code: Niemann-Pick disease, unspecified

A clear reference for the official code description, hierarchy, and related coding information from the FY 2027 U.S. release.

Code definition

Official description

E75.249

Niemann-Pick disease, unspecified

ICD-10-CM diagnosis code · United States clinical modification

Classification

Where E75.249 sits

  1. 1

    Chapter 4

    Endocrine, nutritional and metabolic diseases (E00-E89)

  2. 2

    Section

    Metabolic disorders (E70-E88)

  3. 3

    Category E75

    Disorders of sphingolipid metabolism and other lipid storage disorders

  4. 4

    Subcategory E75.24

    Niemann-Pick disease

  5. 5

    Code E75.249

    Niemann-Pick disease, unspecified

Documentation details

Notes for this code

Inclusion terms

  • Acid sphingomyelinase deficiency (ASMD) NOS

Code first

No “code first” instruction is listed for E75.249.

Use additional code

No “use additional code” instruction is listed for E75.249.

Excludes1

Conditions that should not be reported together with this code.

No Excludes1 note is listed for E75.249.

Excludes2

Conditions not included here that may be reported separately when present.

No Excludes2 note is listed for E75.249.

Transparency

Source and release

Data release

U.S. ICD-10-CM · FY 2027

Effective date

Oct 1, 2026

This reference is generated from Vero’s ICD-10-CM description, hierarchy, and code-note dataset. The visible content and structured data share that source.

Review the CDC/NCHS ICD-10-CM source

Code-specific guidance

Frequently asked questions

What does ICD-10-CM code E75.249 mean?

E75.249 is the FY 2027 U.S. ICD-10-CM code for “Niemann-Pick disease, unspecified.”

Is E75.249 a billable or specific ICD-10-CM code?

Yes. In the FY 2027 reference data used on this page, E75.249 has no child codes and is presented as a billable/specific code. Always confirm the active code set and payer requirements before use.

Where is E75.249 located in ICD-10-CM?

E75.249 is listed in Chapter 4, Endocrine, nutritional and metabolic diseases (E00-E89), within Metabolic disorders (E70-E88) (E70–E88), under category E75, Disorders of sphingolipid metabolism and other lipid storage disorders and subcategory E75.24, Niemann-Pick disease.

What coding notes are listed for E75.249?

Its listed inclusion terms are Acid sphingomyelinase deficiency (ASMD) NOS. No code-first instruction is listed. No Excludes1 note is listed. No Excludes2 note is listed.

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