E75.241 ICD-10-CM Code: Niemann-Pick disease type B
E75.241 is the billable ICD-10-CM code for “Niemann-Pick disease type B” in the FY 2027 U.S. code set, effective Oct 1, 2026.
Official description
E75.241Niemann-Pick disease type B
ICD-10-CM diagnosis code · United States clinical modification
Where E75.241 sits
- 1
Chapter 4
Endocrine, nutritional and metabolic diseases (E00-E89)
- 2
Section
Metabolic disorders (E70-E88)
- 3
Category E75
Disorders of sphingolipid metabolism and other lipid storage disorders
- 4
Subcategory E75.24
Niemann-Pick disease
- 5
Code E75.241
Niemann-Pick disease type B
Notes for this code
Inclusion terms
- Acid sphingomyelinase deficiency type B (ASMD type B)
- Chronic visceral acid sphingomyelinase deficiency
Code first
No “code first” instruction is listed for E75.241.
Use additional code
No “use additional code” instruction is listed for E75.241.
Excludes1
Conditions that should not be reported together with this code.
No Excludes1 note is listed for E75.241.
Excludes2
Conditions not included here that may be reported separately when present.
No Excludes2 note is listed for E75.241.
Source and release
- Data release
- U.S. ICD-10-CM · FY 2027
- Effective date
- Oct 1, 2026
- Publisher
- Vero Scribe Inc.
This reference is generated from Vero’s ICD-10-CM description, hierarchy, and code-note dataset. The visible content and structured data share that source.
Frequently asked questions
What does ICD-10-CM code E75.241 mean?
E75.241 is the FY 2027 U.S. ICD-10-CM code for “Niemann-Pick disease type B.”
Is E75.241 a billable or specific ICD-10-CM code?
Yes. In the FY 2027 reference data used on this page, E75.241 has no child codes and is presented as a billable/specific code. Always confirm the active code set and payer requirements before use.
Where is E75.241 located in ICD-10-CM?
E75.241 is listed in Chapter 4, Endocrine, nutritional and metabolic diseases (E00-E89), within Metabolic disorders (E70-E88) (E70–E88), under category E75, Disorders of sphingolipid metabolism and other lipid storage disorders and subcategory E75.24, Niemann-Pick disease.
What coding notes are listed for E75.241?
Its listed inclusion terms are Acid sphingomyelinase deficiency type B (ASMD type B); Chronic visceral acid sphingomyelinase deficiency. No code-first instruction is listed. No Excludes1 note is listed. No Excludes2 note is listed.