E75.240 ICD-10-CM Code: Niemann-Pick disease type A
A clear reference for the official code description, hierarchy, and related coding information from the FY 2027 U.S. release.
Code definition
Official description
E75.240Niemann-Pick disease type A
ICD-10-CM diagnosis code · United States clinical modification
Classification
Where E75.240 sits
- 1
Chapter 4
Endocrine, nutritional and metabolic diseases (E00-E89)
- 2
Section
Metabolic disorders (E70-E88)
- 3
Category E75
Disorders of sphingolipid metabolism and other lipid storage disorders
- 4
Subcategory E75.24
Niemann-Pick disease
- 5
Code E75.240
Niemann-Pick disease type A
Documentation details
Notes for this code
Inclusion terms
- Acid sphingomyelinase deficiency type A (ASMD type A)
- Infantile neurovisceral acid sphingomyelinase deficiency
Code first
No “code first” instruction is listed for E75.240.
Use additional code
No “use additional code” instruction is listed for E75.240.
Excludes1
Conditions that should not be reported together with this code.
No Excludes1 note is listed for E75.240.
Excludes2
Conditions not included here that may be reported separately when present.
No Excludes2 note is listed for E75.240.
Transparency
Source and release
This reference is generated from Vero’s ICD-10-CM description, hierarchy, and code-note dataset. The visible content and structured data share that source.
Review the CDC/NCHS ICD-10-CM sourceCode-specific guidance
Frequently asked questions
What does ICD-10-CM code E75.240 mean?
E75.240 is the FY 2027 U.S. ICD-10-CM code for “Niemann-Pick disease type A.”
Is E75.240 a billable or specific ICD-10-CM code?
Yes. In the FY 2027 reference data used on this page, E75.240 has no child codes and is presented as a billable/specific code. Always confirm the active code set and payer requirements before use.
Where is E75.240 located in ICD-10-CM?
E75.240 is listed in Chapter 4, Endocrine, nutritional and metabolic diseases (E00-E89), within Metabolic disorders (E70-E88) (E70–E88), under category E75, Disorders of sphingolipid metabolism and other lipid storage disorders and subcategory E75.24, Niemann-Pick disease.
What coding notes are listed for E75.240?
Its listed inclusion terms are Acid sphingomyelinase deficiency type A (ASMD type A); Infantile neurovisceral acid sphingomyelinase deficiency. No code-first instruction is listed. No Excludes1 note is listed. No Excludes2 note is listed.
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Related E75.24 codes
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