E75.01 ICD-10-CM Code: Sandhoff disease

E75.01 is the billable ICD-10-CM code for “Sandhoff disease” in the FY 2027 U.S. code set, effective Oct 1, 2026.

Official description

E75.01

Sandhoff disease

ICD-10-CM diagnosis code · United States clinical modification

Where E75.01 sits

  1. 1

    Chapter 4

    Endocrine, nutritional and metabolic diseases (E00-E89)

  2. 2

    Section

    Metabolic disorders (E70-E88)

  3. 3

    Category E75

    Disorders of sphingolipid metabolism and other lipid storage disorders

  4. 4

    Subcategory E75.0

    GM2 gangliosidosis

  5. 5

    Code E75.01

    Sandhoff disease

Notes for this code

Inclusion terms

No inclusion terms are listed for E75.01.

Code first

No “code first” instruction is listed for E75.01.

Use additional code

No “use additional code” instruction is listed for E75.01.

Excludes1

Conditions that should not be reported together with this code.

No Excludes1 note is listed for E75.01.

Excludes2

Conditions not included here that may be reported separately when present.

No Excludes2 note is listed for E75.01.

Source and release

Data release
U.S. ICD-10-CM · FY 2027
Effective date
Oct 1, 2026

This reference is generated from Vero’s ICD-10-CM description, hierarchy, and code-note dataset. The visible content and structured data share that source.

Frequently asked questions

What does ICD-10-CM code E75.01 mean?

E75.01 is the FY 2027 U.S. ICD-10-CM code for “Sandhoff disease.”

Is E75.01 a billable or specific ICD-10-CM code?

Yes. In the FY 2027 reference data used on this page, E75.01 has no child codes and is presented as a billable/specific code. Always confirm the active code set and payer requirements before use.

Where is E75.01 located in ICD-10-CM?

E75.01 is listed in Chapter 4, Endocrine, nutritional and metabolic diseases (E00-E89), within Metabolic disorders (E70-E88) (E70–E88), under category E75, Disorders of sphingolipid metabolism and other lipid storage disorders and subcategory E75.0, GM2 gangliosidosis.

What coding notes are listed for E75.01?

No inclusion terms are listed for E75.01 in this reference record. No code-first instruction is listed. No Excludes1 note is listed. No Excludes2 note is listed.