U.S. ICD-10-CM · FY 2027

E74.02 ICD-10-CM Code: Pompe disease

A clear reference for the official code description, hierarchy, and related coding information from the FY 2027 U.S. release.

Code definition

Official description

E74.02

Pompe disease

ICD-10-CM diagnosis code · United States clinical modification

Classification

Where E74.02 sits

  1. 1

    Chapter 4

    Endocrine, nutritional and metabolic diseases (E00-E89)

  2. 2

    Section

    Metabolic disorders (E70-E88)

  3. 3

    Category E74

    Other disorders of carbohydrate metabolism

  4. 4

    Subcategory E74.0

    Glycogen storage disease

  5. 5

    Code E74.02

    Pompe disease

Documentation details

Notes for this code

Inclusion terms

  • Cardiac glycogenosis
  • Type II glycogen storage disease

Code first

No “code first” instruction is listed for E74.02.

Use additional code

No “use additional code” instruction is listed for E74.02.

Excludes1

Conditions that should not be reported together with this code.

No Excludes1 note is listed for E74.02.

Excludes2

Conditions not included here that may be reported separately when present.

No Excludes2 note is listed for E74.02.

Transparency

Source and release

Data release

U.S. ICD-10-CM · FY 2027

Effective date

Oct 1, 2026

This reference is generated from Vero’s ICD-10-CM description, hierarchy, and code-note dataset. The visible content and structured data share that source.

Review the CDC/NCHS ICD-10-CM source

Code-specific guidance

Frequently asked questions

What does ICD-10-CM code E74.02 mean?

E74.02 is the FY 2027 U.S. ICD-10-CM code for “Pompe disease.”

Is E74.02 a billable or specific ICD-10-CM code?

Yes. In the FY 2027 reference data used on this page, E74.02 has no child codes and is presented as a billable/specific code. Always confirm the active code set and payer requirements before use.

Where is E74.02 located in ICD-10-CM?

E74.02 is listed in Chapter 4, Endocrine, nutritional and metabolic diseases (E00-E89), within Metabolic disorders (E70-E88) (E70–E88), under category E74, Other disorders of carbohydrate metabolism and subcategory E74.0, Glycogen storage disease.

What coding notes are listed for E74.02?

Its listed inclusion terms are Cardiac glycogenosis; Type II glycogen storage disease. No code-first instruction is listed. No Excludes1 note is listed. No Excludes2 note is listed.

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