E71.4 ICD-10-CM Code: Disorders of carnitine metabolism
A clear reference for the official code description, hierarchy, and related coding information from the FY 2027 U.S. release.
Official description
E71.4Disorders of carnitine metabolism
ICD-10-CM diagnosis code · United States clinical modification
Where E71.4 sits
- 1
Chapter 4
Endocrine, nutritional and metabolic diseases (E00-E89)
- 2
Section
Metabolic disorders (E70-E88)
- 3
Category E71
Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
- 4
Code E71.4
Disorders of carnitine metabolism
Codes under E71.4
E71.4 is a non-billable category. Choose the child code that best matches the documented diagnosis.
Notes for this code
Inclusion terms
No inclusion terms are listed for E71.4.
Code first
No “code first” instruction is listed for E71.4.
Use additional code
No “use additional code” instruction is listed for E71.4.
Excludes1
Conditions that should not be reported together with this code.
- Muscle carnitine palmitoyltransferase deficiency (E71.314)
Excludes2
Conditions not included here that may be reported separately when present.
No Excludes2 note is listed for E71.4.
Source and release
- Data release
- U.S. ICD-10-CM · FY 2027
- Effective date
- Oct 1, 2026
- Publisher
- Vero Scribe Inc.
This reference is generated from Vero’s ICD-10-CM description, hierarchy, and code-note dataset. The visible content and structured data share that source.
Frequently asked questions
What does ICD-10-CM code E71.4 mean?
E71.4 is the FY 2027 U.S. ICD-10-CM code for “Disorders of carnitine metabolism.”
Is E71.4 a billable or specific ICD-10-CM code?
No. E71.4 has more specific child codes in the FY 2027 reference data. Select the code that matches the documentation and confirm the active code set and payer requirements.
Where is E71.4 located in ICD-10-CM?
E71.4 is listed in Chapter 4, Endocrine, nutritional and metabolic diseases (E00-E89), within Metabolic disorders (E70-E88) (E70–E88), under category E71, Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism.
What coding notes are listed for E71.4?
No inclusion terms are listed for E71.4 in this reference record. No code-first instruction is listed. Excludes1 notes: Muscle carnitine palmitoyltransferase deficiency (E71.314). No Excludes2 note is listed.