E71.121 ICD-10-CM Code: Propionic acidemia

E71.121 is the billable ICD-10-CM code for “Propionic acidemia” in the FY 2027 U.S. code set, effective Oct 1, 2026.

Official description

E71.121

Propionic acidemia

ICD-10-CM diagnosis code · United States clinical modification

Where E71.121 sits

  1. 1

    Chapter 4

    Endocrine, nutritional and metabolic diseases (E00-E89)

  2. 2

    Section

    Metabolic disorders (E70-E88)

  3. 3

    Category E71

    Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism

  4. 4

    Subcategory E71.12

    Disorders of propionate metabolism

  5. 5

    Code E71.121

    Propionic acidemia

Notes for this code

Inclusion terms

No inclusion terms are listed for E71.121.

Code first

No “code first” instruction is listed for E71.121.

Use additional code

No “use additional code” instruction is listed for E71.121.

Excludes1

Conditions that should not be reported together with this code.

No Excludes1 note is listed for E71.121.

Excludes2

Conditions not included here that may be reported separately when present.

No Excludes2 note is listed for E71.121.

Source and release

Data release
U.S. ICD-10-CM · FY 2027
Effective date
Oct 1, 2026

This reference is generated from Vero’s ICD-10-CM description, hierarchy, and code-note dataset. The visible content and structured data share that source.

Frequently asked questions

What does ICD-10-CM code E71.121 mean?

E71.121 is the FY 2027 U.S. ICD-10-CM code for “Propionic acidemia.”

Is E71.121 a billable or specific ICD-10-CM code?

Yes. In the FY 2027 reference data used on this page, E71.121 has no child codes and is presented as a billable/specific code. Always confirm the active code set and payer requirements before use.

Where is E71.121 located in ICD-10-CM?

E71.121 is listed in Chapter 4, Endocrine, nutritional and metabolic diseases (E00-E89), within Metabolic disorders (E70-E88) (E70–E88), under category E71, Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism and subcategory E71.12, Disorders of propionate metabolism.

What coding notes are listed for E71.121?

No inclusion terms are listed for E71.121 in this reference record. No code-first instruction is listed. No Excludes1 note is listed. No Excludes2 note is listed.