D81.818 ICD-10-CM Code: Other biotin-dependent carboxylase deficiency
A clear reference for the official code description, hierarchy, and related coding information from the FY 2027 U.S. release.
Code definition
Official description
D81.818Other biotin-dependent carboxylase deficiency
ICD-10-CM diagnosis code · United States clinical modification
Classification
Where D81.818 sits
- 1
Chapter 3
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
- 2
Section
Certain disorders involving the immune mechanism (D80-D89)
- 3
Category D81
Combined immunodeficiencies
- 4
Subcategory D81.81
Biotin-dependent carboxylase deficiency
- 5
Code D81.818
Other biotin-dependent carboxylase deficiency
Documentation details
Notes for this code
Inclusion terms
- Holocarboxylase synthetase deficiency
- Other multiple carboxylase deficiency
Code first
No “code first” instruction is listed for D81.818.
Use additional code
No “use additional code” instruction is listed for D81.818.
Excludes1
Conditions that should not be reported together with this code.
No Excludes1 note is listed for D81.818.
Excludes2
Conditions not included here that may be reported separately when present.
No Excludes2 note is listed for D81.818.
Transparency
Source and release
This reference is generated from Vero’s ICD-10-CM description, hierarchy, and code-note dataset. The visible content and structured data share that source.
Review the CDC/NCHS ICD-10-CM sourceCode-specific guidance
Frequently asked questions
What does ICD-10-CM code D81.818 mean?
D81.818 is the FY 2027 U.S. ICD-10-CM code for “Other biotin-dependent carboxylase deficiency.”
Is D81.818 a billable or specific ICD-10-CM code?
Yes. In the FY 2027 reference data used on this page, D81.818 has no child codes and is presented as a billable/specific code. Always confirm the active code set and payer requirements before use.
Where is D81.818 located in ICD-10-CM?
D81.818 is listed in Chapter 3, Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89), within Certain disorders involving the immune mechanism (D80-D89) (D80–D89), under category D81, Combined immunodeficiencies and subcategory D81.81, Biotin-dependent carboxylase deficiency.
What coding notes are listed for D81.818?
Its listed inclusion terms are Holocarboxylase synthetase deficiency; Other multiple carboxylase deficiency. No code-first instruction is listed. No Excludes1 note is listed. No Excludes2 note is listed.
Keep exploring
Related D81.81 codes
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